Homozygous carnitine palmitoyltransferase 1b (muscle isoform) deficiency is lethal in the mouse
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Mutation in CPT1C Associated With Pure Autosomal Dominant Spastic ParaplegiaA general introduction to the biochemistry of mitochondrial fatty acid β-oxidationFatty acid metabolism and the basis of brown adipose tissue functionMitochondrial dysfunction in fatty acid oxidation disorders: insights from human and animal studiesMitochondrial long chain fatty acid beta-oxidation in man and mouseAdipose fatty acid oxidation is required for thermogenesis and potentiates oxidative stress-induced inflammationThe brown and brite adipocyte marker Cox7a1 is not required for non-shivering thermogenesis in miceEffects of epigallocatechin-3-gallate on thermogenesis and mitochondrial biogenesis in brown adipose tissues of diet-induced obese mice.The role of mitochondrial DNA copy number in mammalian fertility.Mitochondrial fatty acid oxidation disorders: pathophysiological studies in mouse modelsCarnitine palmitoyltransferase 1A (CPT1A): a transcriptional target of PAX3-FKHR and mediates PAX3-FKHR-dependent motility in alveolar rhabdomyosarcoma cellsCarnitine Palmitoyltransferase 1b Deficiency Protects Mice from Diet-Induced Insulin ResistanceMetabolomic profiling reveals a role for CPT1c in neuronal oxidative metabolismCarnitine Palmitoyltransferase 1b Deficient Mice Develop Severe Insulin Resistance After Prolonged High Fat Diet Feeding.Carnitine Palmitoyltransferase 1 Increases Lipolysis, UCP1 Protein Expression and Mitochondrial Activity in Brown Adipocytes.Carnitine palmitoyltransferase-1b deficiency aggravates pressure overload-induced cardiac hypertrophy caused by lipotoxicityMitochondrial Dysfunction may explain symptom variation in Phelan-McDermid Syndrome.The Ablation of Mitochondrial Protein Phosphatase Pgam5 Confers Resistance Against Metabolic Stress.Hepatic Fatty Acid Oxidation Restrains Systemic Catabolism during Starvation.Requirement for the Mitochondrial Pyruvate Carrier in Mammalian Development Revealed by a Hypomorphic Allelic Series.Skeletal muscle-specific CPT1 deficiency elevates lipotoxic intermediates but preserves insulin sensitivity.NAT8L (N-acetyltransferase 8-like) accelerates lipid turnover and increases energy expenditure in brown adipocytes.Mitochondrial dysfunction in non-alcoholic fatty liver disease and insulin resistance: cause or consequence?Brown fat fuel utilization and thermogenesisGood and bad consequences of altered fatty acid metabolism in heart failure: evidence from mouse models.Mitochondrial disease in 22q13 duplication syndrome.Inhibition of carnitine palmitoyltransferase-1 activity alleviates insulin resistance in diet-induced obese mice.Impaired thermogenesis and sharp increases in plasma triglyceride levels in GPIHBP1-deficient mice during cold exposure.
P2860
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P2860
Homozygous carnitine palmitoyltransferase 1b (muscle isoform) deficiency is lethal in the mouse
description
2007 nî lūn-bûn
@nan
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
2007年论文
@zh
2007年论文
@zh-cn
name
Homozygous carnitine palmitoyl ...... iciency is lethal in the mouse
@ast
Homozygous carnitine palmitoyl ...... iciency is lethal in the mouse
@en
type
label
Homozygous carnitine palmitoyl ...... iciency is lethal in the mouse
@ast
Homozygous carnitine palmitoyl ...... iciency is lethal in the mouse
@en
prefLabel
Homozygous carnitine palmitoyl ...... iciency is lethal in the mouse
@ast
Homozygous carnitine palmitoyl ...... iciency is lethal in the mouse
@en
P2093
P2860
P1476
Homozygous carnitine palmitoyl ...... iciency is lethal in the mouse
@en
P2093
Charles L Hoppel
Doug A Hamm
J Daniel Sharer
Janos Kerner
Philip A Wood
Shaonin Ji
Trenton R Schoeb
Wallace S H Chick
P2860
P304
P356
10.1016/J.YMGME.2007.10.006
P577
2007-11-19T00:00:00Z