Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease - Wikidata - awgldk - TriplyDB

Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

http://www.wikidata.org/entity/Q36650540

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Animal models of GM2 gangliosidosis: utility and limitations Therapeutic response in feline sandhoff disease despite immunity to intracranial gene therapy.A single intravenous rAAV injection as late as P20 achieves efficacious and sustained CNS Gene therapy in Canavan mice.Influence of a ketogenic diet, fish-oil, and calorie restriction on plasma metabolites and lipids in C57BL/6J mice.Multi-system disorders of glycosphingolipid and ganglioside metabolism Bis(monoacylglycero)phosphate: a secondary storage lipid in the gangliosidoses.Clinical utility of neuronal cells directly converted from fibroblasts of patients for neuropsychiatric disorders: studies of lysosomal storage diseases and channelopathy AAV-mediated gene delivery in a feline model of Sandhoff disease corrects lysosomal storage in the central nervous system.Protease-resistant modified human β-hexosaminidase B ameliorates symptoms in GM2 gangliosidosis model Reversibility of neuropathology in Tay-Sachs-related diseases.Glucose-dependent de novo lipogenesis in B lymphocytes: a requirement for atp-citrate lyase in lipopolysaccharide-induced differentiation.Widespread correction of central nervous system disease after intracranial gene therapy in a feline model of Sandhoff disease.Adeno-associated virus-mediated expression of β-hexosaminidase prevents neuronal loss in the Sandhoff mouse brain.Cerebral organoids derived from Sandhoff disease induced pluripotent stem cells exhibit impaired neurodifferentiation.Ethylenedioxy-PIP2 oxalate reduces ganglioside storage in juvenile Sandhoff disease mice.Sex-Related Abnormalities in Substantia Nigra Lipids in Parkinson's Disease.

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P2860

Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

http://www.wikidata.org/entity/Q36650540

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2008 nî lūn-bûn

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2008年の論文

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2008年論文

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2008年论文

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name

Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

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Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

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Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

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Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

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Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

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Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

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Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease

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Nancy R Cox

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Rena C Baek

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P2860

Evolution of the brain and intelligence

A simple method for the isolation and purification of total lipides from animal tissues

NSAIDs increase survival in the Sandhoff disease mouse: synergy with N-butyldeoxynojirimycin

Enzyme alterations and lipid storage in three variants of Tay-Sachs disease

Brain sizes, surfaces, and neuronal sizes of the cortex cerebri: a stereological investigation of man and his variability and a comparison with some mammals (primates, whales, marsupials, insectivores, and one elephant)

Degradation of G(M1) and G(M2) by mammalian sialidases

Mouse models of Tay-Sachs and Sandhoff diseases differ in neurologic phenotype and ganglioside metabolism

Specificity of mouse GM2 activator protein and beta-N-acetylhexosaminidases A and B. Similarities and differences with their human counterparts in the catabolism of GM2

Effective gene therapy in an authentic model of Tay-Sachs-related diseases

Dysmyelinogenesis in animal model of GM1 gangliosidosis.

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