Alteration of retinal rod outer segment membrane fluidity in a rat model of Smith-Lemli-Opitz syndrome.
about
The Effect of Small Molecules on Sterol Homeostasis: Measuring 7-Dehydrocholesterol in Dhcr7-Deficient Neuro2a Cells and Human FibroblastsIon-current-based proteomic profiling of the retina in a rat model of Smith-Lemli-Opitz syndrome.Cone ERG responses in patients with Smith-Lemli-Opitz Syndrome (SLOS).Malformation syndromes caused by disorders of cholesterol synthesis.Role of membrane integrity on G protein-coupled receptors: Rhodopsin stability and function.Raman Spectroscopic Imaging of Cholesterol and Docosahexaenoic Acid Distribution in the Retinal Rod Outer Segment.Pathogenesis, Epidemiology, Diagnosis and Clinical Aspects of Smith-Lemli-Opitz Syndrome.7-dehydrocholesterol efficiently supports Ret signaling in a mouse model of Smith-Opitz-Lemli syndrome.Retinal degeneration in a rat model of Smith-Lemli-Opitz Syndrome: thinking beyond cholesterol deficiency.Differential cytotoxic effects of 7-dehydrocholesterol-derived oxysterols on cultured retina-derived cells: Dependence on sterol structure, cell type, and density.Smith-Lemli-Opitz syndrome.Prevention of Retinal Degeneration in a Rat Model of Smith-Lemli-Opitz Syndrome.Adrenal function in Smith-Lemli-Opitz syndrome.
P2860
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P2860
Alteration of retinal rod outer segment membrane fluidity in a rat model of Smith-Lemli-Opitz syndrome.
description
2008 nî lūn-bûn
@nan
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
2008年论文
@zh
2008年论文
@zh-cn
name
Alteration of retinal rod oute ...... of Smith-Lemli-Opitz syndrome.
@ast
Alteration of retinal rod oute ...... of Smith-Lemli-Opitz syndrome.
@en
type
label
Alteration of retinal rod oute ...... of Smith-Lemli-Opitz syndrome.
@ast
Alteration of retinal rod oute ...... of Smith-Lemli-Opitz syndrome.
@en
prefLabel
Alteration of retinal rod oute ...... of Smith-Lemli-Opitz syndrome.
@ast
Alteration of retinal rod oute ...... of Smith-Lemli-Opitz syndrome.
@en
P2093
P2860
P1476
Alteration of retinal rod oute ...... of Smith-Lemli-Opitz syndrome.
@en
P2093
Drake C Mitchell
Kathleen Boesze-Battaglia
Laura Greeley
Michael J Richards
Monika Damek-Poprawa
Richard S Brush
Robert E Anderson
Steven J Fliesler
P2860
P304
P356
10.1194/JLR.M800031-JLR200
P577
2008-03-14T00:00:00Z