The effect of mutated mitochondrial ribosomal proteins S16 and S22 on the assembly of the small and large ribosomal subunits in human mitochondria.
about
Pentatricopeptide repeat domain protein 3 associates with the mitochondrial small ribosomal subunit and regulates translationHuman G-proteins, ObgH1 and Mtg1, associate with the large mitochondrial ribosome subunit and are involved in translation and assembly of respiratory complexesProperties of the C-terminal tail of human mitochondrial inner membrane protein Oxa1L and its interactions with mammalian mitochondrial ribosomesCryo-EM structure of the small subunit of the mammalian mitochondrial ribosomeRibosome. The complete structure of the 55S mammalian mitochondrial ribosomeA bifunctional protein regulates mitochondrial protein synthesisMutation in MRPS34 compromises protein synthesis and causes mitochondrial dysfunctionLeveraging existing data sets to generate new insights into Alzheimer's disease biology in specific patient subsets.NAD+-dependent deacetylase SIRT3 regulates mitochondrial protein synthesis by deacetylation of the ribosomal protein MRPL10.Analysis of the functional consequences of lethal mutations in mitochondrial translational elongation factorsERAL1 is associated with mitochondrial ribosome and elimination of ERAL1 leads to mitochondrial dysfunction and growth retardation.Mutation in mitochondrial ribosomal protein MRPS22 leads to Cornelia de Lange-like phenotype, brain abnormalities and hypertrophic cardiomyopathy.Mechanism of protein biosynthesis in mammalian mitochondria.Dichloroacetate reverses the hypoxic adaptation to bevacizumab and enhances its antitumor effects in mouse xenografts.The FOXP2-Driven Network in Developmental Disorders and NeurodegenerationBiallelic Mutations in MRPS34 Lead to Instability of the Small Mitoribosomal Subunit and Leigh Syndrome.MRPS27 is a pentatricopeptide repeat domain protein required for the translation of mitochondrially encoded proteins.Mutation in mitochondrial ribosomal protein S7 (MRPS7) causes congenital sensorineural deafness, progressive hepatic and renal failure and lactic acidemia.Molecular adaptation in the world's deepest-living animal: Insights from transcriptome sequencing of the hadal amphipod Hirondellea gigas.Kinetics and Mechanism of Mammalian Mitochondrial Ribosome Assembly.Mutation in a mitochondrial ribosomal protein causes increased sensitivity to oxygen with decreased longevity in the nematode Caenorhabditis elegans.Bi-allelic Mutations in the Mitochondrial Ribosomal Protein MRPS2 Cause Sensorineural Hearing Loss, Hypoglycemia, and Multiple OXPHOS Complex Deficiencies.
P2860
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P2860
The effect of mutated mitochondrial ribosomal proteins S16 and S22 on the assembly of the small and large ribosomal subunits in human mitochondria.
description
2008 nî lūn-bûn
@nan
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
2008年论文
@zh
2008年论文
@zh-cn
name
The effect of mutated mitochon ...... ubunits in human mitochondria.
@en
type
label
The effect of mutated mitochon ...... ubunits in human mitochondria.
@en
prefLabel
The effect of mutated mitochon ...... ubunits in human mitochondria.
@en
P2093
P2860
P1433
P1476
The effect of mutated mitochon ...... subunits in human mitochondria
@en
P2093
Chaya Miller
Domenick Grasso
Linda L Spremulli
Md Emdadul Haque
P2860
P304
P356
10.1016/J.MITO.2008.04.004
P50
P577
2008-04-30T00:00:00Z