Liver transplantation for classical maple syrup urine disease: long-term follow-up in 37 patients and comparative United Network for Organ Sharing experience - Wikidata - awgldk - TriplyDB

Liver transplantation for classical maple syrup urine disease: long-term follow-up in 37 patients and comparative United Network for Organ Sharing experience

Liver transplantation for classical maple syrup urine disease: long-term follow-up in 37 patients and comparative United Network for Organ Sharing experience

http://www.wikidata.org/entity/Q36900920

about

Branched-chain amino acids in metabolic signalling and insulin resistance Pediatric liver transplantation for urea cycle disorders and organic acidemias: United Network for Organ Sharing data for 2002-2012.Brain-blood amino acid correlates following protein restriction in murine maple syrup urine disease.Successful domino liver transplantation in maple syrup urine disease using a related living donor.Branched-chain amino acid metabolism: from rare Mendelian diseases to more common disorders.Quality of life, psychological adjustment, and adaptive functioning of patients with intoxication-type inborn errors of metabolism - a systematic review New potential cell source for hepatocyte transplantation: discarded livers from metabolic disease liver transplants.Developmental Defects of Caenorhabditis elegans Lacking Branched-chain α-Ketoacid Dehydrogenase Are Mainly Caused by Monomethyl Branched-chain Fatty Acid Deficiency.Two consecutive partial liver transplants in a patient with Classic Maple Syrup Urine Disease Barriers to transplantation in adults with inborn errors of metabolism.Biochemical correlates of neuropsychiatric illness in maple syrup urine disease Successful Domino Liver Transplantation from a Patient with Methylmalonic Acidemia.Adipose transplant for inborn errors of branched chain amino acid metabolism in mice.Therapeutic hepatocyte transplant for inherited metabolic disorders: functional considerations, recent outcomes and future prospects.Liver transplantation for pediatric inherited metabolic disorders: Considerations for indications, complications, and perioperative management.Living donor liver transplantation from a heterozygous parent for classical maple syrup urine disease.Genetic, hematological, and immunological disorders transmissible with liver transplantation.Enzymes involved in branched-chain amino acid metabolism in humans.Long-term metabolic follow-up and clinical outcome of 35 patients with maple syrup urine disease.Liver transplant in ethylmalonic encephalopathy: a new treatment for an otherwise fatal disease.Maple syrup urine disease: mechanisms and management.Acute Metabolic Crises in Maple Syrup Urine Disease After Liver Transplantation from a Related Heterozygous Living Donor The first case of domino-split-liver transplantation in maple syrup urine disease.Host conditioning and rejection monitoring in hepatocyte transplantation in humans.Successful living donor liver transplantation for classical maple syrup urine disease.Maple syrup urine disease (MSUD): a case with long-term follow-up after liver transplantation.A case of classical maple syrup urine disease that was successfully managed by living donor liver transplantation.Liver transplantation may prevent neurodevelopmental deterioration in high-risk patients with urea cycle disorders.Heterozygote to homozygote related living donor liver transplantation in maple syrup urine disease: a case report.Disorders of branched chain amino acid metabolism.Perioperative management of living donor related liver transplantation in an infant for Maple syrup urine disease

P2860

Q28249276-6E5B6168-E0D1-429F-A921-7C9258AD814F Q30679633-69CF4469-4226-44A0-AB2A-80ACAD033693 Q33617530-BC650D64-32D0-4035-9B52-FD8DD900CB43 Q33861034-20CB3AA7-72E5-469D-A7ED-61E6B8B63A8F Q34222287-60D4B56B-3688-40D7-A589-BB324B7EA984 Q34446836-0CD1010A-1D21-4540-8E77-BB713C60018E Q34673712-A262253A-5841-445B-A978-22D5B9BC1319 Q36548413-702E8CC6-6555-415A-86E0-22FC1941BE7D Q36571556-5DC38029-DBAD-42D9-9C74-57EB5F57A2C7 Q36590903-1F59DB96-00F1-4E38-9E24-2F0927AFD6A3 Q36733516-D7FEC179-7324-4B3F-84B0-BD0D488B59FF Q37329311-241AD3C5-5697-459B-B115-5E6FCADECDA8 Q37640465-EA05C2B7-E2BE-4299-8064-D289F8233673 Q37684677-266934C3-4822-4924-9702-9CDDBFE27525 Q38872573-615DEBCC-D5B6-4508-83D8-F19C3F7882DE Q39036137-752169D9-C8BB-40B0-8E33-DE09A127220C Q39152643-D002F0D9-EFA9-49D2-82FF-FF86B155ABA5 Q39190517-5DFDF123-55D7-4FFE-AE82-FE8D1DF0860D Q40047282-8235A5A8-37EC-40BA-93BD-B75D90A7BD36 Q40886181-31EE8B63-507E-4038-9396-6E338F4C4241 Q41355931-3EEE6363-58C7-4AAD-917A-66D192C3D8F9 Q41911110-D5642A08-6C3D-43BF-991B-725D7BDF575D Q47741953-CBAEF87A-FA60-469E-9694-A2F8638DC5CD Q47906882-9C5F0EC9-641B-4A70-8730-D80ECC62BCD8 Q47998929-7212F244-CD92-424F-898A-4F0477D8BDF0 Q48002467-CF711715-4C53-4936-BB81-7F610A2794D1 Q48281291-1176A9EC-84B1-446C-A767-330F4C8CE2D7 Q48286981-F10A3A7A-AFAF-47E0-984E-DB8EF4A6F261 Q53809440-0B4A9257-6FF9-47B3-A899-656CB2145B9A Q54966951-43F8AD79-E5CA-4EA7-8B1F-F65B11D33BFF Q59133346-037655A7-31A3-44B4-9EA0-D910811A2372

P2860

Liver transplantation for classical maple syrup urine disease: long-term follow-up in 37 patients and comparative United Network for Organ Sharing experience

http://www.wikidata.org/entity/Q36900920

description

2011 nî lūn-bûn

@nan

2011年の論文

@ja

2011年論文

@yue

2011年論文

@zh-hant

2011年論文

@zh-hk

2011年論文

@zh-mo

2011年論文

@zh-tw

2011年论文

@wuu

2011年论文

@zh

2011年论文

@zh-cn

name

Liver transplantation for clas ...... k for Organ Sharing experience

@en

type

label

Liver transplantation for clas ...... k for Organ Sharing experience

@en

prefLabel

Liver transplantation for clas ...... k for Organ Sharing experience

@en

P1433

Q36900920-4FE4BAF4-385E-42F7-95C5-6E92B7B4289C

P1476

Q36900920-C06A04B0-708D-4EAF-BBB6-88C2E5484371

P2093

Q36900920-3B788846-964E-42C1-82D0-A6951BD228BE

Q36900920-818D39ED-13F1-4FE2-87B9-01E3092407FA

Q36900920-966B209A-B14C-44EE-AC1A-B9BDFF2EE4AA

Q36900920-C8403DF4-E091-4EAC-90F5-FCD685088629

Q36900920-EF4A88A5-F082-4521-BAC7-9431DDFCAF56

Q36900920-F23481EA-3676-4496-ACAC-F83B74764C29

Q36900920-F9A80F5B-24C4-45DB-A24C-9CA89CD06C0D

Q36900920-FF7382EB-17F4-4E80-A2DB-F359E678F2BF

P2860

Q36900920-0724E77C-9967-4BA1-8C73-E776654670EB

Q36900920-15D3F46C-1A5A-44AD-9785-C62047F7EEBC

Q36900920-2D67DA8D-AB73-4685-BEBB-01A5B3F8F0AE

Q36900920-3E202668-3599-4959-9AE0-CD7BC4E9AC94

Q36900920-3FCF60E2-12BF-4173-B6DB-113446DBFEAF

Q36900920-4582B6B6-9DD5-46A3-B35B-A8261F019712

Q36900920-6FBB239D-9642-4BD2-B651-EB5E9F845DDA

Q36900920-74C505BB-46A5-48CA-B937-154AA497A1B5

Q36900920-75B557D8-ED9A-47D6-8BBC-FC93EFE2E6F3

Q36900920-7742B0E9-1390-433B-AB17-27886880EFD5

P304

Q36900920-67E0001E-0F7C-4928-95BE-C539309B901E

P31

Q36900920-E373A653-A8EB-4289-A71A-87730423E8CA

P356

Q36900920-16917A9D-FF56-4AC1-A466-BB8D7FD85F81

P407

Q36900920-BCF332EA-0647-4DE4-AD55-4CBFE7433C5B

P433

Q36900920-FF2FC948-1D88-4F8B-A754-DED4F1292564

P478

Q36900920-ABEB75C0-1FAE-4505-87D3-9B5D197409C5

P50

Q36900920-AE1BF3AA-F233-4F27-ABD5-1F77CCD7EE90

Q36900920-F96417C6-AF6F-43D2-97E0-3C2A33D807B6

P577

Q36900920-04D65050-A7A7-45B0-BCA2-DBBCA358284B

P5875

Q36900920-7D777105-BA1B-405B-95AD-76CAB807BF52

P698

Q36900920-6CDE2E35-C1BF-4929-B638-ACC33339B69C

P921

Q36900920-9A25362D-478A-467F-9D1B-4461C02623AC

P932

Q36900920-7FAA1F3E-5959-4BAA-AA30-4C08AA34FC9F

P356

J.JPEDS.2011.06.033

P1433

The Journal of Pediatrics

P1476

Liver transplantation for clas ...... k for Organ Sharing experience

@en

P2093

Benjamin Shneider

http://www.w3.org/2001/XMLSchema#string

D Holmes Morton

http://www.w3.org/2001/XMLSchema#string

Diana Shellmer

http://www.w3.org/2001/XMLSchema#string

Geoffrey Bond

http://www.w3.org/2001/XMLSchema#string

Kevin A Strauss

http://www.w3.org/2001/XMLSchema#string

Kyle Soltys

http://www.w3.org/2001/XMLSchema#string

Navdeep Nayyar

http://www.w3.org/2001/XMLSchema#string

Rakesh Sindhi

http://www.w3.org/2001/XMLSchema#string

P2860

Lifelong elimination of hyperbilirubinemia in the Gunn rat with a single injection of helper-dependent adenoviral vector

Review of hepatocyte transplantation.

Indications for pediatric liver transplantation.

Efficient, long-term hepatic gene transfer using clinically relevant HDAd doses by balloon occlusion catheter delivery in nonhuman primates

Pediatric liver transplantation in metabolic disease: clinical decision making.

Cognitive and adaptive functioning after liver transplantation for maple syrup urine disease: a case series.

Classical maple syrup urine disease and brain development: principles of management and formula design

Dual mechanism of brain injury and novel treatment strategy in maple syrup urine disease

Stable correction of maple syrup urine disease in cells from a Mennonite patient by retroviral-mediated gene transfer.

Hepatocyte transplantation (HTx) corrects selected neurometabolic abnormalities in murine intermediate maple syrup urine disease (iMSUD).

P304

116-21.e1

http://www.w3.org/2001/XMLSchema#string

P31

scholarly article

P356

10.1016/J.JPEDS.2011.06.033

http://www.w3.org/2001/XMLSchema#string

P407

P433

1

http://www.w3.org/2001/XMLSchema#string

P478

160

http://www.w3.org/2001/XMLSchema#string

P50

George Mazariegos

P577

2011-08-11T00:00:00Z

http://www.w3.org/2001/XMLSchema#dateTime

P5875

51569381

http://www.w3.org/2001/XMLSchema#string

P698

21839471

http://www.w3.org/2001/XMLSchema#string

P921

liver transplantation

P932

3671923

http://www.w3.org/2001/XMLSchema#string