Fibrillin-rich microfibrils: Structural determinants of morphogenetic and homeostatic events.
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Essential role for fibrillin-2 in zebrafish notochord and vascular morphogenesisStructure and interdomain interactions of a hybrid domain: a disulphide-rich module of the fibrillin/LTBP superfamily of matrix proteinsCorneal stroma microfibrilsMechanotransduction and extracellular matrix homeostasisGeneration of heterozygous fibrillin-1 mutant cloned pigs from genome-edited foetal fibroblastsLTBP2 null mutations in an autosomal recessive ocular syndrome with megalocornea, spherophakia, and secondary glaucomaLosartan therapy in adults with Marfan syndrome: study protocol of the multi-center randomized controlled COMPARE trialUnraveling the mechanism of elastic fiber assembly: The roles of short fibulinsDrug-based therapies for vascular disease in Marfan syndrome: from mouse models to human patients.The importance of elastin to aortic development in mice.Cystathionine beta-synthase null homocystinuric mice fail to exhibit altered hemostasis or lowering of plasma homocysteine in response to betaine treatment.Inflammation aggravates disease severity in Marfan syndrome patients.Rare and common variants in extracellular matrix gene Fibrillin 2 (FBN2) are associated with macular degeneration.Comparative immunolocalisation of fibrillin-1 and perlecan in the human foetal, and HS-deficient hspg2 exon 3 null mutant mouse intervertebral disc.The prevalence of nine genetic disorders in a dog population from Belgium, the Netherlands and Germany.Decreased elastic energy storage, not increased material stiffness, characterizes central artery dysfunction in fibulin-5 deficiency independent of sexADAMTSL6β protein rescues fibrillin-1 microfibril disorder in a Marfan syndrome mouse model through the promotion of fibrillin-1 assembly.Cardiac remodeling in the mouse model of Marfan syndrome develops into two distinctive phenotypesPerturbations of the cerebrovascular matrisome: A convergent mechanism in small vessel disease of the brain?Latent TGF-β binding protein 4 promotes elastic fiber assembly by interacting with fibulin-5.Deficiency in microfibril-associated glycoprotein-1 leads to complex phenotypes in multiple organ systemsFibrillin assembly requires fibronectin.Loss of Elastic Fiber Integrity Compromises Common Carotid Artery Function: Implications for Vascular Aging.Vascular extracellular matrix and arterial mechanics.The microfibril-associated glycoproteins (MAGPs) and the microfibrillar niche.The extracellular matrix of the dermis: flexible structures with dynamic functions.Extracellular matrix administration as a potential therapeutic strategy for periodontal ligament regeneration.Drosophila MMP2 regulates the matrix molecule faulty attraction (Frac) to promote motor axon targeting in Drosophila.Angiotensin receptor I stimulates osteoprogenitor proliferation through TGFβ-mediated signaling.The development of the vasculature and its extracellular matrix: a gradual process defined by sequential cellular and matrix remodeling events.Colocalization in vivo and association in vitro of perlecan and elastin.Differential stage-dependent regulation of prostatic epithelial morphogenesis by Hedgehog signaling.Intrinsic cardiomyopathy in Marfan syndrome: results from in-vivo and ex-vivo studies of the Fbn1C1039G/+ model and longitudinal findings in humans.
P2860
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P2860
Fibrillin-rich microfibrils: Structural determinants of morphogenetic and homeostatic events.
description
2007 nî lūn-bûn
@nan
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
2007年论文
@zh
2007年论文
@zh-cn
name
Fibrillin-rich microfibrils: S ...... enetic and homeostatic events.
@en
type
label
Fibrillin-rich microfibrils: S ...... enetic and homeostatic events.
@en
prefLabel
Fibrillin-rich microfibrils: S ...... enetic and homeostatic events.
@en
P356
P1476
Fibrillin-rich microfibrils: S ...... enetic and homeostatic events.
@en
P2093
Francesco Ramirez
Harry C Dietz
P304
P356
10.1002/JCP.21189
P577
2007-11-01T00:00:00Z