Lysosomal membrane permeability stimulates protein aggregate formation in neurons of a lysosomal disease
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Unfolded Protein Response and Macroautophagy in Alzheimer's, Parkinson's and Prion DiseasesLysosomal storage diseases and the heat shock response: convergences and therapeutic opportunitiesAtaxia is the major neuropathological finding in arylsulfatase G-deficient mice: similarities and dissimilarities to Sanfilippo disease (mucopolysaccharidosis type III).AAV gene transfer delays disease onset in a TPP1-deficient canine model of the late infantile form of Batten disease.Lysosomal dysfunction and impaired autophagy in a novel mouse model deficient for the lysosomal membrane protein Cln7Heat shock protein-based therapy as a potential candidate for treating the sphingolipidoses.Evidence for aberrant astrocyte hemichannel activity in Juvenile Neuronal Ceroid Lipofuscinosis (JNCL).Astrocytes and lysosomal storage diseases.Autophagy in neuronal cells: general principles and physiological and pathological functions.Prion degradation pathways: Potential for therapeutic intervention.Lysosomal membrane permeabilization in cell death: new evidence and implications for health and disease.Lysosome and endoplasmic reticulum quality control pathways in Niemann-Pick type C disease.Contribution of membrane trafficking perturbation to retinal toxicity.The first genetically confirmed Japanese patient with mucolipidosis type IV.A tripeptidyl peptidase 1 is a binding partner of the Golgi pH regulator (GPHR) in Dictyostelium.Acid Ceramidase Deficiency in Mice Results in a Broad Range of Central Nervous System Abnormalities.Loss of CLN7 results in depletion of soluble lysosomal proteins and impaired mTOR reactivation.Hypoxia-ischemia alters distribution of lysosomal proteins in rat cortex and hippocampus
P2860
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P2860
Lysosomal membrane permeability stimulates protein aggregate formation in neurons of a lysosomal disease
description
2013 nî lūn-bûn
@nan
2013年の論文
@ja
2013年論文
@yue
2013年論文
@zh-hant
2013年論文
@zh-hk
2013年論文
@zh-mo
2013年論文
@zh-tw
2013年论文
@wuu
2013年论文
@zh
2013年论文
@zh-cn
name
Lysosomal membrane permeabilit ...... neurons of a lysosomal disease
@en
type
label
Lysosomal membrane permeabilit ...... neurons of a lysosomal disease
@en
prefLabel
Lysosomal membrane permeabilit ...... neurons of a lysosomal disease
@en
P2093
P2860
P1476
Lysosomal membrane permeabilit ...... neurons of a lysosomal disease
@en
P2093
Gloria Stephney
Jakub Sikora
Kostantin Dobrenis
Matthew C Micsenyi
Steven U Walkley
P2860
P304
10815-10827
P356
10.1523/JNEUROSCI.0987-13.2013
P407
P577
2013-06-01T00:00:00Z