Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype. - Wikidata - awgldk - TriplyDB

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

http://www.wikidata.org/entity/Q37049924

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C. elegans in high-throughput drug discovery Long-term clinical outcomes following treatment with alpha 1-proteinase inhibitor for COPD associated with alpha-1 antitrypsin deficiency: a look at the evidence.The aggregation-prone intracellular serpin SRP-2 fails to transit the ER in Caenorhabditis elegans.Oxidative stress and calcium dysregulation by palmitate in type 2 diabetes.Worming our way to novel drug discovery with the Caenorhabditis elegans proteostasis network, stress response and insulin-signaling pathways.Characteristics of Chronic Obstructive Pulmonary Disease (COPD) Patients Reporting Alpha-1 Antitrypsin Deficiency in the WebMD Lung Health Check Database.The Intersection Of Aging Biology and The Pathobiology of Lung Diseases: A Joint NHLBI/NIA Workshop.Could Autophagy Induced by Misfolded Mutant α1 -Antitrypsin Z in Synovitis Explain the Association of α1 -Antitrypsin Z With Increased Anti-Citrullinated Protein Antibody Production in Rheumatoid Arthritis? Comment on the Article by McCarthy et al.Alpha-1 antitrypsin deficiency: outstanding questions and future directions.

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Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

http://www.wikidata.org/entity/Q37049924

description

article científic

@ca

article scientifique

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articolo scientifico

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artigo científico

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bilimsel makale

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scientific article published on 08 May 2013

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vedecký článok

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vetenskaplig artikel

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videnskabelig artikel

@da

vědecký článek

@cs

name

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

@en

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

@nl

type

label

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

@en

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

@nl

prefLabel

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

@en

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

@nl

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J.JPEDS.2013.03.077

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The Journal of Pediatrics

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Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

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David H Perlmutter

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Gary A Silverman

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Stephen C Pak

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Automated high-content live animal drug screening using C. elegans expressing the aggregation prone serpin α1-antitrypsin Z

Intravenous alpha-1 antitrypsin augmentation therapy for treating patients with alpha-1 antitrypsin deficiency and lung disease

Characterization of an ERAD gene as VPS30/ATG6 reveals two alternative and functionally distinct protein quality control pathways: one for soluble Z variant of human alpha-1 proteinase inhibitor (A1PiZ) and another for aggregates of A1PiZ.

Exercise-induced BCL2-regulated autophagy is required for muscle glucose homeostasis

Histone deacetylase inhibitor (HDACi) suberoylanilide hydroxamic acid (SAHA)-mediated correction of α1-antitrypsin deficiency

Targeted gene correction of α1-antitrypsin deficiency in induced pluripotent stem cells

Small molecules block the polymerization of Z alpha1-antitrypsin and increase the clearance of intracellular aggregates

Effectiveness of specific RNA-mediated interference through ingested double-stranded RNA in Caenorhabditis elegans

Chemical and biological approaches for adapting proteostasis to ameliorate protein misfolding and aggregation diseases: progress and prognosis

Adapting proteostasis for disease intervention

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320-326

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scholarly article

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10.1016/J.JPEDS.2013.03.077

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