Connexin defects underlie arrhythmogenic right ventricular cardiomyopathy in a novel mouse model.
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Disease mutations in desmoplakin inhibit Cx43 membrane targeting mediated by desmoplakin-EB1 interactions.Cardiac disease and arrhythmogenesis: Mechanistic insights from mouse modelsCell junctions in the specialized conduction system of the heartStriatins as plaque molecules of zonulae adhaerentes in simple epithelia, of tessellate junctions in stratified epithelia, of cardiac composite junctions and of various size classes of lateral adherens junctions in cultures of epithelia- and carcinoMechanotransduction in cardiac hypertrophy and failure.New Cell Adhesion Molecules in Human Ischemic Cardiomyopathy. PCDHGA3 Implications in Decreased Stroke Volume and Ventricular Dysfunction.Prolactin mediates effects of chronic psychological stress on induction of fibrofatty cells in the heart.Myocyte-fibroblast communication in cardiac fibrosis and arrhythmias: Mechanisms and model systems.Identification of rare variants of DSP gene in sudden unexplained nocturnal death syndrome in the southern Chinese Han populationRemodeling of cell-cell junctions in arrhythmogenic cardiomyopathyDesmosomes in the heart: a review of clinical and mechanistic analyses.Arrhythmogenic cardiomyopathy: a disease of intercalated discs.Cardiac cytoarchitecture - why the "hardware" is important for heart function!Resveratrol protects the loss of connexin 43 induced by ethanol exposure in neonatal mouse cardiomyocytes.Murine Electrophysiological Models of Cardiac Arrhythmogenesis.Intermediate Filaments and the Plasma Membrane.Genetic and epigenetic regulation of arrhythmogenic cardiomyopathy.Animal models of arrhythmogenic right ventricular cardiomyopathy: what have we learned and where do we go? Insight for therapeutics.Unmasking the molecular link between arrhythmogenic cardiomyopathy and Brugada syndrome.Desmosomal junctions are necessary for adult sinus node function.MicroRNA-130a Regulation of Desmocollin 2 in a Novel Model of Arrhythmogenic Cardiomyopathy.Distinct Cellular Basis for Early Cardiac Arrhythmias, the Cardinal Manifestation of Arrhythmogenic Cardiomyopathy, and the Skin Phenotype of Cardiocutaneous Syndromes.Arrhythmogenic cardiomyopathy: pathology, genetics, and concepts in pathogenesis.The conduction system and expressions of hyperpolarization-activated cyclic nucleotide-gated cation channel 4 and connexin43 expressions in the hearts of fetal day 13 mice.Liganded retinoic acid X receptor α represses connexin 43 through a potential retinoic acid response element in the promoter region.Molecular disturbance underlies to arrhythmogenic cardiomyopathy induced by transgene content, age and exercise in a truncated PKP2 mouse model.
P2860
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P2860
Connexin defects underlie arrhythmogenic right ventricular cardiomyopathy in a novel mouse model.
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article científic
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article scientifique
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articolo scientifico
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artigo científico
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bilimsel makale
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scientific article published on 09 October 2013
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vedecký článok
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vetenskaplig artikel
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videnskabelig artikel
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vědecký článek
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name
Connexin defects underlie arrh ...... opathy in a novel mouse model.
@en
Connexin defects underlie arrh ...... opathy in a novel mouse model.
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type
label
Connexin defects underlie arrh ...... opathy in a novel mouse model.
@en
Connexin defects underlie arrh ...... opathy in a novel mouse model.
@nl
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Connexin defects underlie arrh ...... opathy in a novel mouse model.
@en
Connexin defects underlie arrh ...... opathy in a novel mouse model.
@nl
P2093
P2860
P356
P1476
Connexin defects underlie arrh ...... opathy in a novel mouse model.
@en
P2093
Adam T Wright
Allan Castaneda
Andrew D McCulloch
Emily Pfeiffer
Farah Sheikh
Jeffrey H Omens
Joyce Chuang
Katherine Banares
Kirk L Peterson
Kunfu Ouyang
P2860
P304
P356
10.1093/HMG/DDT508
P577
2013-10-09T00:00:00Z