Allele-specific Col1a1 silencing reduces mutant collagen in fibroblasts from Brtl mouse, a model for classical osteogenesis imperfecta.
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Bone Material Properties in Osteogenesis Imperfecta.The chaperone activity of 4PBA ameliorates the skeletal phenotype of Chihuahua, a zebrafish model for dominant osteogenesis imperfecta.Pharmacological and biological therapeutic strategies for osteogenesis imperfecta.Osteogenesis imperfecta and therapeutics.New frontiers for dominant osteogenesis imperfecta treatment: gene/cellular therapy approachesTreatment options for osteogenesis imperfecta
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Allele-specific Col1a1 silencing reduces mutant collagen in fibroblasts from Brtl mouse, a model for classical osteogenesis imperfecta.
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article científic
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article scientifique
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articolo scientifico
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artigo científico
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bilimsel makale
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scientific article published on 11 September 2013
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vedecký článok
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vetenskaplig artikel
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videnskabelig artikel
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vědecký článek
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name
Allele-specific Col1a1 silenci ...... sical osteogenesis imperfecta.
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Allele-specific Col1a1 silenci ...... sical osteogenesis imperfecta.
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label
Allele-specific Col1a1 silenci ...... sical osteogenesis imperfecta.
@en
Allele-specific Col1a1 silenci ...... sical osteogenesis imperfecta.
@nl
prefLabel
Allele-specific Col1a1 silenci ...... sical osteogenesis imperfecta.
@en
Allele-specific Col1a1 silenci ...... sical osteogenesis imperfecta.
@nl
P2093
P2860
P356
P1476
Allele-specific Col1a1 silenci ...... sical osteogenesis imperfecta.
@en
P2093
Antonella Forlino
Antonio Rossi
Blandine Lieubeau
Joan C Marini
Julie Rousseau
Roberta Gioia
Valerie Trichet
P2860
P2888
P304
P356
10.1038/EJHG.2013.198
P577
2013-09-11T00:00:00Z