Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
about
Malfolded protein structure and proteostasis in lung diseases.ERAD defects and the HFE-H63D variant are associated with increased risk of liver damages in Alpha 1-Antitrypsin DeficiencyBlue journal conference. Aging and susceptibility to lung disease.Golgi localization of ERManI defines spatial separation of the mammalian glycoprotein quality control system.Therapeutic targeting of misfolding and conformational change in α1-antitrypsin deficiency.Glycoprotein folding and quality-control mechanisms in protein-folding diseasesViral serpin therapeutics from concept to clinic.Measuring the Effect of Histone Deacetylase Inhibitors (HDACi) on the Secretion and Activity of Alpha-1 Antitrypsin.Protein folding: Protection from the outside.
P2860
Q30353585-E3D619AA-5DA1-4CF0-9857-E0FC0DC579CCQ33803215-11EB5392-99F1-420D-B8CD-C4F7FE951F81Q35153456-5D88E3F3-CE8D-488B-AB2F-F6E057C9C1FCQ35160707-E29C5E49-7D00-4DA3-8D9B-15B85C6B0FF5Q35214289-DE72DEAC-C578-4817-BC53-E2B49270C50DQ37621073-C7AC9B26-FC08-4414-A84C-7C1C9CBE65C2Q37891258-6173521D-660C-4D18-AAEF-27354262FB9EQ47160647-E48ABD12-5B51-49DF-A9C8-F7D1CF963732Q54367095-292451B0-5131-4DA7-8A2E-6E6FDE2885DC
P2860
Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
description
2010 nî lūn-bûn
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2010年の論文
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2010年学术文章
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2010年学术文章
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name
Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
@en
Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
@nl
type
label
Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
@en
Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
@nl
prefLabel
Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
@en
Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
@nl
P2093
P2860
P1476
Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
@en
P2093
Juliana J Conkright
Marion Bouchecareilh
William E Balch
P2860
P304
P356
10.1513/PATS.201001-016AW
P577
2010-11-01T00:00:00Z