Mitochondrial respiratory complex I defects in Fanconi anemia.
about
Treatment of FANCA cells with resveratrol and N-acetylcysteine: a comparative studyFanconi anemia protein FANCD2 is activated by AICAR, a modulator of AMPK and cellular energy metabolismDysregulated Ca2+ homeostasis in Fanconi anemia cells.Evaluation of energy metabolism and calcium homeostasis in cells affected by Shwachman-Diamond syndrome.AMP-activated protein kinase is involved in the activation of the Fanconi anemia/BRCA pathway in response to DNA interstrand crosslinks.Mitochondrial dysfunction: a neglected component of skin diseases.Concentration-dependent metabolic effects of metformin in healthy and Fanconi anemia lymphoblast cells.How I manage patients with Fanconi anaemia.Involvement of FANCD2 in Energy Metabolism via ATP5α.Fancd2 in vivo interaction network reveals a non-canonical role in mitochondrial function.Fanconi anemia: from DNA repair to metabolism.Inhibition of Metalloproteinase Activity in FANCA Is Linked to Altered Oxygen Metabolism
P2860
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P2860
Mitochondrial respiratory complex I defects in Fanconi anemia.
description
article científic
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article scientifique
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articol științific
@ro
articolo scientifico
@it
artigo científico
@gl
artigo científico
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artigo científico
@pt-br
artikel ilmiah
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artikull shkencor
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artículo científico
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name
Mitochondrial respiratory complex I defects in Fanconi anemia.
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type
label
Mitochondrial respiratory complex I defects in Fanconi anemia.
@en
prefLabel
Mitochondrial respiratory complex I defects in Fanconi anemia.
@en
P2093
P50
P1476
Mitochondrial respiratory complex I defects in Fanconi anemia
@en
P2093
Carlo Dufour
Daniele Vaccaro
Martina Bartolucci
Paola Cuccarolo
Paolo Degan
P304
P356
10.1016/J.MOLMED.2013.07.008
P577
2013-08-06T00:00:00Z