Neurological damage in MSUD: the role of oxidative stress.
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In Vivo NMR Studies of the Brain with Hereditary or Acquired Metabolic Disorders.Brain-blood amino acid correlates following protein restriction in murine maple syrup urine disease.Altered Metabolic Profiles Associate with Toxicity in SOD1G93A Astrocyte-Neuron Co-Cultures.Branched-chain amino acid metabolism: from rare Mendelian diseases to more common disorders.Developmental Defects of Caenorhabditis elegans Lacking Branched-chain α-Ketoacid Dehydrogenase Are Mainly Caused by Monomethyl Branched-chain Fatty Acid Deficiency.Regulation of PP2Cm expression by miRNA-204/211 and miRNA-22 in mouse and human cellsDisturbance of redox homeostasis as a contributing underlying pathomechanism of brain and liver alterations in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency.Neurocognitive profiles in MSUD school-age patients.Branched-Chain Amino Acids and Brain Metabolism.Long-term metabolic follow-up and clinical outcome of 35 patients with maple syrup urine disease.L-carnitine Prevents Oxidative Stress in the Brains of Rats Subjected to a Chemically Induced Chronic Model of MSUD.Investigation of inflammatory profile in MSUD patients: benefit of L-carnitine supplementation.BCAA Metabolism and NH3 Homeostasis.Evaluation of dynamic thiol/disulphide homeostasis as a novel indicator of oxidative stress in maple syrup urine disease patients under treatment.Altered Redox Homeostasis in Branched-Chain Amino Acid Disorders, Organic Acidurias, and Homocystinuria.
P2860
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P2860
Neurological damage in MSUD: the role of oxidative stress.
description
2013 nî lūn-bûn
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2013年の論文
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2013年学术文章
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2013年学术文章
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2013年学术文章
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2013年学术文章
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2013年学术文章
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2013年學術文章
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2013年學術文章
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2013年學術文章
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name
Neurological damage in MSUD: the role of oxidative stress.
@en
type
label
Neurological damage in MSUD: the role of oxidative stress.
@en
prefLabel
Neurological damage in MSUD: the role of oxidative stress.
@en
P2093
P2860
P1476
Neurological damage in MSUD: the role of oxidative stress
@en
P2093
Angela Sitta
Carmen R Vargas
Caroline P Mescka
Graziela S Ribas
Moacir Wajner
P2860
P2888
P304
P356
10.1007/S10571-013-0002-0
P577
2013-11-13T00:00:00Z
P5875
P6179
1030130953