about
The Unfolded Protein Response and the Role of Protein Disulfide Isomerase in NeurodegenerationGolgi Fragmentation in ALS Motor Neurons. New Mechanisms Targeting Microtubules, Tethers, and Transport VesiclesALS Patient Stem Cells for Unveiling Disease Signatures of Motoneuron Susceptibility: Perspectives on the Deadly Mitochondria, ER Stress and Calcium TriadGenetic disorders coupled to ROS deficiencyMechanisms of aging-related proteinopathies in Caenorhabditis elegansPrion-like Mechanism in Amyotrophic Lateral Sclerosis: are Protein Aggregates the Key?Endoplasmic reticulum stress and inflammation in the central nervous systemAn ALS-Associated Mutant SOD1 Rapidly Suppresses KCNT1 (Slack) Na+-Activated K+ Channels in Aplysia NeuronsTDP-43 toxicity proceeds via calcium dysregulation and necrosis in aging Caenorhabditis elegans motor neurons.Elevated mRNA-levels of distinct mitochondrial and plasma membrane Ca(2+) transporters in individual hypoglossal motor neurons of endstage SOD1 transgenic mice.C9ORF72 GGGGCC Expanded Repeats Produce Splicing Dysregulation which Correlates with Disease Severity in Amyotrophic Lateral SclerosisGuanabenz Treatment Accelerates Disease in a Mutant SOD1 Mouse Model of ALS.Disturbance of endoplasmic reticulum proteostasis in neurodegenerative diseases.Worming forward: amyotrophic lateral sclerosis toxicity mechanisms and genetic interactions in Caenorhabditis elegans.Fishing for causes and cures of motor neuron disorders.Old versus New Mechanisms in the Pathogenesis of ALS.Advances in the Development of Disease-Modifying Treatments for Amyotrophic Lateral Sclerosis.The role of endoplasmic reticulum stress in neurodegenerative disease.Cysteine Modifications in the Pathogenesis of ALS.Control of mRNA Translation in ALS ProteinopathyERp57 in neurodegeneration and regeneration.ALS-linked protein disulfide isomerase variants cause motor dysfunction.Identification of rare protein disulfide isomerase gene variants in amyotrophic lateral sclerosis patients.Deciphering genetic interactions between ALS genes using C. elegans.Plekhg5-regulated autophagy of synaptic vesicles reveals a pathogenic mechanism in motoneuron disease.Autophagy meets fused in sarcoma-positive stress granules.Glycoursodeoxycholic acid reduces matrix metalloproteinase-9 and caspase-9 activation in a cellular model of superoxide dismutase-1 neurodegeneration.Sex specific activation of the ERα axis of the mitochondrial UPR (UPRmt) in the G93A-SOD1 mouse model of familial ALS.Piperine ameliorates SCA17 neuropathology by reducing ER stress.Polymorphisms in protein disulfide isomerase are associated with sporadic amyotrophic lateral sclerosis in the Chinese Han population.Exploring microRNA Biomarker for Amyotrophic Lateral Sclerosis.
P2860
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P2860
description
2013 nî lūn-bûn
@nan
2013年の論文
@ja
2013年学术文章
@wuu
2013年学术文章
@zh-cn
2013年学术文章
@zh-hans
2013年学术文章
@zh-my
2013年学术文章
@zh-sg
2013年學術文章
@yue
2013年學術文章
@zh
2013年學術文章
@zh-hant
name
ER Dysfunction and Protein Folding Stress in ALS.
@en
type
label
ER Dysfunction and Protein Folding Stress in ALS.
@en
prefLabel
ER Dysfunction and Protein Folding Stress in ALS.
@en
P2093
P2860
P356
P1476
ER Dysfunction and Protein Folding Stress in ALS.
@en
P2093
Claudio Hetz
Danilo B Medinas
Soledad Matus
Vicente Valenzuela
P2860
P304
P356
10.1155/2013/674751
P577
2013-11-13T00:00:00Z