about
Fatal familial insomnia with abnormal signals on routine MRI: a case report and literature review.Current evidence on the transmissibility of chronic wasting disease prions to humans-A systematic review.Fatal Familial Insomnia: Clinical Aspects and Molecular Alterations.Genetic prion disease: Experience of a rapidly progressive dementia center in the United States and a review of the literature.The copper transport-associated protein Ctr4 can form prion-like epigenetic determinants in Schizosaccharomyces pombe.Transmissibility of Gerstmann-Sträussler-Scheinker syndrome in rodent models: New insights into the molecular underpinnings of prion infectivity.The celecoxib derivatives AR-12 and AR-14 induce autophagy and clear prion-infected cells from prions.Recombinant PrP and Its Contribution to Research on Transmissible Spongiform Encephalopathies.Applications of the real-time quaking-induced conversion assay in diagnosis, prion strain-typing, drug pre-screening and other amyloidopathies.The Structure of PrPSc Prions.A Chinese patient of P102L Gerstmann-Sträussler-Scheinker disease contains three other disease-associated mutations in SYNE1.Glycosylation Significantly Inhibits the Aggregation of Human Prion Protein and Decreases Its Cytotoxicity
P2860
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P2860
description
2016 nî lūn-bûn
@nan
2016年の論文
@ja
2016年論文
@yue
2016年論文
@zh-hant
2016年論文
@zh-hk
2016年論文
@zh-mo
2016年論文
@zh-tw
2016年论文
@wuu
2016年论文
@zh
2016年论文
@zh-cn
name
Hereditary Human Prion Diseases: an Update.
@en
type
label
Hereditary Human Prion Diseases: an Update.
@en
prefLabel
Hereditary Human Prion Diseases: an Update.
@en
P2093
P2860
P1476
Hereditary Human Prion Diseases: an Update.
@en
P2093
Ellen Gelpi
Franc Llorens
Isidre Ferrer
Kathrin Dittmar
Matthias Schmitz
Walter J Schulz-Schaeffer
P2860
P2888
P304
P356
10.1007/S12035-016-9918-Y
P577
2016-06-20T00:00:00Z
P6179
1016109371