Biogenesis of Weibel-Palade bodies in von Willebrand's disease variants with impaired von Willebrand factor intrachain or interchain disulfide bond formation.
about
von Willebrand disease: clinical and laboratory lessons learned from the large von Willebrand disease studiesWeibel-Palade bodies: a window to von Willebrand disease.Insights into pathological mechanisms of missense mutations in C-terminal domains of von Willebrand factor causing qualitative or quantitative von Willebrand disease.Aberrant disulphide bonding contributes to the ER retention of alpha1-antitrypsin deficiency variants.Cysteines as Redox Molecular Switches and Targets of Disease.Formation of platelet-binding von Willebrand factor strings on non-endothelial cells.Angiogenic characteristics of blood outgrowth endothelial cells from patients with von Willebrand diseaseStorage and secretion of naturally occurring von Willebrand factor A domain variants
P2860
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P2860
Biogenesis of Weibel-Palade bodies in von Willebrand's disease variants with impaired von Willebrand factor intrachain or interchain disulfide bond formation.
description
2011 nî lūn-bûn
@nan
2011年の論文
@ja
2011年学术文章
@wuu
2011年学术文章
@zh-cn
2011年学术文章
@zh-hans
2011年学术文章
@zh-my
2011年学术文章
@zh-sg
2011年學術文章
@yue
2011年學術文章
@zh
2011年學術文章
@zh-hant
name
Biogenesis of Weibel-Palade bo ...... hain disulfide bond formation.
@en
Biogenesis of Weibel-Palade bo ...... hain disulfide bond formation.
@nl
type
label
Biogenesis of Weibel-Palade bo ...... hain disulfide bond formation.
@en
Biogenesis of Weibel-Palade bo ...... hain disulfide bond formation.
@nl
prefLabel
Biogenesis of Weibel-Palade bo ...... hain disulfide bond formation.
@en
Biogenesis of Weibel-Palade bo ...... hain disulfide bond formation.
@nl
P2093
P2860
P1433
P1476
Biogenesis of Weibel-Palade bo ...... hain disulfide bond formation.
@en
P2093
Dafna J Groeneveld
Guy Cosemans
Jan Voorberg
Jeroen Eikenboom
Jiong-Wei Wang
Karine M Valentijn
Pieter H Reitsma
Richard J Dirven
P2860
P304
P356
10.3324/HAEMATOL.2011.057216
P577
2011-12-29T00:00:00Z