Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

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Matrix Metalloproteinases and Tissue Inhibitor of Metalloproteinases in Inflammation and Fibrosis of Skeletal Muscles

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Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

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2016 nî lūn-bûn

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2016年の論文

@ja

2016年論文

@yue

2016年論文

@zh-hant

2016年論文

@zh-hk

2016年論文

@zh-mo

2016年論文

@zh-tw

2016年论文

@wuu

2016年论文

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2016年论文

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name

Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

@en

Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

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Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

@en

Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

@nl

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Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

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Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

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P1476

Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

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P2093

Alice Bondi

http://www.w3.org/2001/XMLSchema#string

Cesare Faldini

http://www.w3.org/2001/XMLSchema#string

Francesca Sardone

http://www.w3.org/2001/XMLSchema#string

Francesco Traina

http://www.w3.org/2001/XMLSchema#string

Nadir Mario Maraldi

http://www.w3.org/2001/XMLSchema#string

Patrizia Sabatelli

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P2860

Three novel collagen VI chains, alpha4(VI), alpha5(VI), and alpha6(VI)

MMP mediated degradation of type VI collagen is highly associated with liver fibrosis--identification and validation of a novel biochemical marker assay

A mouse model for dominant collagen VI disorders: heterozygous deletion of Col6a3 Exon 16

Collagen fibril formation

Type VI collagen in extracellular, 100-nm periodic filaments and fibrils: identification by immunoelectron microscopy.

Biglycan organizes collagen VI into hexagonal-like networks resembling tissue structures.

Three-dimensional architecture of collagen type VI in the human trabecular meshwork

Zebrafish models of collagen VI-related myopathies

New molecular mechanism for Ullrich congenital muscular dystrophy: a heterozygous in-frame deletion in the COL6A1 gene causes a severe phenotype.

Characterization of a rare case of Ullrich congenital muscular dystrophy due to truncating mutations within the COL6A1 gene C-terminal domain: a case report.

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131

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scholarly article

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10.3389/FNAGI.2016.00131

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P478

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Spartaco Santi

Luciano Merlini

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2016-06-08T00:00:00Z

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27375477

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extracellular matrix

Ullrich congenital muscular dystrophy

P932

4896961

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Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

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Tendon Extracellular Matrix Alterations in Ullrich Congenital Muscular Dystrophy.

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P1433

P1476

P2093

P2860

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P698

P921

P932

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P1433

P1476

P2093

P2860

P304

P31

P356

P478

P50

P577

P698

P921

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