Retinobenzaldehydes as proper-trafficking inducers of folding-defective P23H rhodopsin mutant responsible for retinitis pigmentosa.
about
Endoplasmic reticulum stress and the unfolded protein responses in retinal degeneration.A High-Throughput Drug Screening Strategy for Detecting Rhodopsin P23H Mutant Rescue and Degradation.Explant cultures of Rpe65-/- mouse retina: a model to investigate cone opsin trafficking.Rescue of mutant rhodopsin traffic by metformin-induced AMPK activation accelerates photoreceptor degeneration.Gene therapy in animal models of autosomal dominant retinitis pigmentosaTranscriptome profiling of NIH3T3 cell lines expressing opsin and the P23H opsin mutant identifies candidate drugs for the treatment of retinitis pigmentosa.Ligand channel in pharmacologically stabilized rhodopsin.A novel small molecule chaperone of rod opsin and its potential therapy for retinal degeneration.
P2860
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P2860
Retinobenzaldehydes as proper-trafficking inducers of folding-defective P23H rhodopsin mutant responsible for retinitis pigmentosa.
description
2010 nî lūn-bûn
@nan
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
2010年论文
@zh
2010年论文
@zh-cn
name
Retinobenzaldehydes as proper- ...... ible for retinitis pigmentosa.
@en
Retinobenzaldehydes as proper- ...... ible for retinitis pigmentosa.
@nl
type
label
Retinobenzaldehydes as proper- ...... ible for retinitis pigmentosa.
@en
Retinobenzaldehydes as proper- ...... ible for retinitis pigmentosa.
@nl
prefLabel
Retinobenzaldehydes as proper- ...... ible for retinitis pigmentosa.
@en
Retinobenzaldehydes as proper- ...... ible for retinitis pigmentosa.
@nl
P2093
P1476
Retinobenzaldehydes as proper- ...... ible for retinitis pigmentosa.
@en
P2093
Kenji Ohgane
Kosuke Dodo
Yuichi Hashimoto
P304
P356
10.1016/J.BMC.2010.08.014
P407
P577
2010-08-11T00:00:00Z