Inherited complex I deficiency is associated with faster protein diffusion in the matrix of moving mitochondria. - Wikidata - awgldk - TriplyDB

Inherited complex I deficiency is associated with faster protein diffusion in the matrix of moving mitochondria.

Inherited complex I deficiency is associated with faster protein diffusion in the matrix of moving mitochondria.

http://www.wikidata.org/entity/Q40000489

about

Downscaling the analysis of complex transmembrane signaling cascades to closed attoliter volumes Complex patterns of mitochondrial dynamics in human pancreatic cells revealed by fluorescent confocal imaging.Biophysical properties of mitochondrial fusion events in pancreatic beta-cells and cardiac cells unravel potential control mechanisms of its selectivity.Solute diffusion is hindered in the mitochondrial matrix Mitofusins are required for angiogenic function and modulate different signaling pathways in cultured endothelial cells.Multiplexed high-content analysis of mitochondrial morphofunction using live-cell microscopy.Mouse models for nuclear DNA-encoded mitochondrial complex I deficiency.Metabolic manipulators: a well founded strategy to combat mitochondrial dysfunction.Quantifying intracellular dynamics using fluorescence fluctuation spectroscopy.In vitro characterization of mitochondrial function and structure in rat and human cells with a deficiency of the NADH: ubiquinone oxidoreductase Ndufc2 subunit.

P2860

Q27309957-B55B76B3-2453-4E35-9638-FB8E7C4D6E6A Q33433158-7D3102CA-6757-45FA-97FD-477C163C347F Q34085652-5477CBF9-8B76-406F-9870-4484C8A8FC06 Q35008267-D91D172C-6D7E-4B8D-B55E-1CF86781DB90 Q35529133-9F14A853-D47C-4F40-BE33-63F443B2D63C Q36112717-28827B35-10A7-4627-B403-5BB9951BC13E Q37682674-9E4D5931-1900-48FA-8669-F101C13A64F9 Q37776434-501E6E75-C21B-413E-884C-64D26DE7EBDC Q38178152-6081426D-2098-4CE7-9AF9-4FD11D834B34 Q46295972-6462B601-9592-4235-B9F9-DD897BCF3CAD

P2860

Inherited complex I deficiency is associated with faster protein diffusion in the matrix of moving mitochondria.

http://www.wikidata.org/entity/Q40000489

description

2008 nî lūn-bûn

@nan

2008年の論文

@ja

2008年学术文章

@wuu

2008年学术文章

@zh-cn

2008年学术文章

@zh-hans

2008年学术文章

@zh-my

2008年学术文章

@zh-sg

2008年學術文章

@yue

2008年學術文章

@zh

2008年學術文章

@zh-hant

name

Inherited complex I deficiency ...... matrix of moving mitochondria.

@en

type

label

Inherited complex I deficiency ...... matrix of moving mitochondria.

@en

prefLabel

Inherited complex I deficiency ...... matrix of moving mitochondria.

@en

P1433

Q40000489-0147A6B7-C29A-4D7C-B560-620D1E1E7876

P1476

Q40000489-FD6E86BB-6DF8-4CD3-989B-EBF46EDC06E3

P2093

Q40000489-172ED685-DBDD-4EA0-B55C-68676127CB9D

Q40000489-22A3940A-669D-49BC-85C5-2D91C33E255F

Q40000489-599FD29E-6D1B-440E-BB21-A4397AD8A81D

Q40000489-9DB71B40-02C5-447E-9E8E-907F36E38D31

Q40000489-B1CB929D-6B8C-4B53-942B-DB2FEA7AEC7F

Q40000489-DA704C4B-6638-4F82-BD1A-BBC8C1B52C04

Q40000489-FF024B50-2D70-48CD-9065-BA53715FB4FC

P2860

Q40000489-04B9C388-C05B-492E-BC13-E04455C37E6D

Q40000489-05D12CFD-CCBC-4846-AE8C-6F42940EE41E

Q40000489-084C46F0-7DAF-45A6-82C2-2EA651955F6D

Q40000489-0CDBB31F-9CAD-4176-88F0-D911D52C28BB

Q40000489-1E54D12E-A102-4C1E-B855-BAE18658E783

Q40000489-20426B3B-615B-4032-A5E1-3AF0DEA8B59C

Q40000489-20C242F5-7AAD-4709-8771-79A7F4E0A177

Q40000489-27229CF7-20D8-40F5-833A-63B9B50DF251

Q40000489-27AF5BC1-72DA-4AFE-951C-EBE451A8C2F7

Q40000489-2829FCC1-6159-4180-884C-4DE2227F7850

P304

Q40000489-E225E18D-FC76-4F4F-8C2A-1E5D5230F0EA

P31

Q40000489-92D09CE7-1F7C-4217-BEF5-F2F59DDFBF28

P356

Q40000489-958AB5A8-1D3D-4A36-A0DF-A05D4630EF0D

P433

Q40000489-F7D18CAA-44ED-4176-AD99-BE83E6F1431E

P478

Q40000489-D169819F-AF06-4208-B569-860AE753EFBA

P50

Q40000489-54439748-EC33-47B2-94EA-858FFA3A282E

P577

Q40000489-5ACB138C-B29B-4735-BEE0-02B28B23D041

P698

Q40000489-80F1C75F-B157-4BF3-ACDF-CF288ECBEAC7

P921

Q40000489-C34A4FB6-F7DE-4C85-B356-0DB7A4E4291F

P356

AJPCELL.00079.2008

P1433

American Journal of Physiology - Cell Physiology

P1476

Inherited complex I deficiency ...... matrix of moving mitochondria

@en

P2093

Felix Distelmaier

http://www.w3.org/2001/XMLSchema#string

Jack Fransen

http://www.w3.org/2001/XMLSchema#string

Jan A M Smeitink

http://www.w3.org/2001/XMLSchema#string

Mark A Hink

http://www.w3.org/2001/XMLSchema#string

Mietske Wijers

http://www.w3.org/2001/XMLSchema#string

Sjoerd Verkaart

http://www.w3.org/2001/XMLSchema#string

Werner J H Koopman

http://www.w3.org/2001/XMLSchema#string

P2860

The first nuclear-encoded complex I mutation in a patient with Leigh syndrome.

Mutant NDUFV2 subunit of mitochondrial complex I causes early onset hypertrophic cardiomyopathy and encephalopathy

NDUFS6 mutations are a novel cause of lethal neonatal mitochondrial complex I deficiency

C6ORF66 is an assembly factor of mitochondrial complex I

Differences in assembly or stability of complex I and other mitochondrial OXPHOS complexes in inherited complex I deficiency

Demonstration of a new pathogenic mutation in human complex I deficiency: a 5-bp duplication in the nuclear gene encoding the 18-kD (AQDQ) subunit.

Large-scale deletion and point mutations of the nuclear NDUFV1 and NDUFS1 genes in mitochondrial complex I deficiency

A molecular chaperone for mitochondrial complex I assembly is mutated in a progressive encephalopathy.

Mutant NDUFS3 subunit of mitochondrial complex I causes Leigh syndrome

Human CIA30 is involved in the early assembly of mitochondrial complex I and mutations in its gene cause disease

P304

C1124-32

http://www.w3.org/2001/XMLSchema#string

P31

scholarly article

P356

10.1152/AJPCELL.00079.2008

http://www.w3.org/2001/XMLSchema#string

P433

5

http://www.w3.org/2001/XMLSchema#string

P478

294

http://www.w3.org/2001/XMLSchema#string

P50

Peter H Willems

P577

2008-03-19T00:00:00Z

http://www.w3.org/2001/XMLSchema#dateTime

P698

18353897

http://www.w3.org/2001/XMLSchema#string

P921