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Neurodegeneration and Epilepsy in a Zebrafish Model of CLN3 Disease (Batten Disease)Distinct early molecular responses to mutations causing vLINCL and JNCL presage ATP synthase subunit C accumulation in cerebellar cellsCLN3p impacts galactosylceramide transport, raft morphology, and lipid contentAutophagy is disrupted in a knock-in mouse model of juvenile neuronal ceroid lipofuscinosisProgress in the Development of Small Molecule Therapeutics for the Treatment of Neuronal Ceroid Lipofuscinoses (NCLs).Lithium rescues the impaired autophagy process in CbCln3(Δex7/8/Δex7/8) cerebellar cells and reduces neuronal vulnerability to cell death via IMPase inhibition.Association between CLN3 (Neuronal Ceroid Lipofuscinosis, CLN3 Type) Gene Expression and Clinical Characteristics of Breast Cancer PatientsJuvenile neuronal ceroid lipofuscinosis (JNCL) and the eye.Lysosomal storage diseases--the horizon expands.Flunarizine rescues reduced lifespan in CLN3 triple knock-out Caenorhabditis elegans model of batten disease.Flow injection tandem mass spectrometric measurement of ceramides of multiple chain lengths in biological samples.Mutant batten disease protein says "no" to unsaturated fats.Microglia in juvenile neuronal ceroid lipofuscinosis are primed toward a pro-inflammatory phenotype.Mitochondrial aberrations in mucolipidosis Type IV.Flupirtine derivatives as potential treatment for the neuronal ceroid lipofuscinoses
P2860
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P2860
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年論文
@yue
2005年論文
@zh-hant
2005年論文
@zh-hk
2005年論文
@zh-mo
2005年論文
@zh-tw
2005年论文
@wuu
2005年论文
@zh
2005年论文
@zh-cn
name
Cell death pathways in juvenile Batten disease.
@en
type
label
Cell death pathways in juvenile Batten disease.
@en
prefLabel
Cell death pathways in juvenile Batten disease.
@en
P1433
P1476
Cell death pathways in juvenile Batten disease.
@en
P2093
D A Persaud-Sawin
R-M N Boustany
P2860
P2888
P304
P356
10.1007/S10495-005-0733-6
P577
2005-10-01T00:00:00Z