about
Activation of the epithelial sodium channel (ENaC) by the alkaline protease from Pseudomonas aeruginosaOrganic solutes rescue the functional defect in delta F508 cystic fibrosis transmembrane conductance regulator.The cystic fibrosis-causing mutation deltaF508 affects multiple steps in cystic fibrosis transmembrane conductance regulator biogenesis.ESCRT-dependent targeting of plasma membrane localized KCa3.1 to the lysosomesRegulation of ABCC6 trafficking and stability by a conserved C-terminal PDZ-like sequenceCFTR regulatory region interacts with NBD1 predominantly via multiple transient helicesA protein sequence that can encode native structure by disfavoring alternate conformations.NMR evidence for differential phosphorylation-dependent interactions in WT and DeltaF508 CFTR.Molecular modeling tools and approaches for CFTR and cystic fibrosis.Solubilizing Mutations Used to Crystallize One CFTR Domain Attenuate the Trafficking and Channel Defects Caused by the Major Cystic Fibrosis MutationStructural analysis reveals pathomechanisms associated with pseudoxanthoma elasticum-causing mutations in the ABCC6 transporter
P50
Q28492964-7AD62E0B-E05E-4DAE-8DCE-7F2DCC289E50Q33973031-D7DCD1D8-9E56-45D6-9BEC-237C5ACAEFB6Q34285307-AC5F1942-F23B-40DE-9461-92A6E4DC46C1Q34304952-4930763A-FB13-4A29-B21C-654B64BDBF34Q35170848-05514F3D-EDB6-49F3-A87D-0A5F7C587F9DQ37618800-F653CBE4-F04E-48B2-8F03-2E549125EBFDQ40739635-20B46E1F-7978-4F94-B7F8-21CB07871DAFQ41882930-BE115895-957F-4D99-BAD1-40D7D8D8F3B3Q46057580-166D4793-A8BB-4D2B-AC25-3D6DA234399AQ57762321-A1075ED6-C13E-4525-B056-4C4936A91A08Q91183763-998F2B8E-B697-473C-8EC3-51DA6340660A
P50
description
hulumtues
@sq
researcher
@en
wetenschapper
@nl
հետազոտող
@hy
name
Patrick H Thibodeau
@ast
Patrick H Thibodeau
@en
Patrick H Thibodeau
@es
Patrick H Thibodeau
@nl
Patrick H Thibodeau
@sl
type
label
Patrick H Thibodeau
@ast
Patrick H Thibodeau
@en
Patrick H Thibodeau
@es
Patrick H Thibodeau
@nl
Patrick H Thibodeau
@sl
prefLabel
Patrick H Thibodeau
@ast
Patrick H Thibodeau
@en
Patrick H Thibodeau
@es
Patrick H Thibodeau
@nl
Patrick H Thibodeau
@sl
P106
P21
P31
P496
0000-0002-6790-144X