about
A novel host defense system of airways is defective in cystic fibrosisThe lactoperoxidase system links anion transport to host defense in cystic fibrosisBinding of protegrin-1 to Pseudomonas aeruginosa and Burkholderia cepacia.The Evolution of Cystic Fibrosis CareRecent advances in cystic fibrosisRole of aquaporin water channels in airway fluid transport, humidification, and surface liquid hydrationThe elements of life and medicinesThe expansion of autologous adipose-derived stem cells in vitro for the functional reconstruction of nasal mucosal tissue.Osmotic water permeabilities of cultured, well-differentiated normal and cystic fibrosis airway epitheliaNanodelivery in airway diseases: challenges and therapeutic applications.Status of gene therapy for cystic fibrosis lung diseaseImpact of multidrug-resistant organisms on patients considered for lung transplantation.Non-specific activation of the epithelial sodium channel by the CFTR chloride channelCystic fibrosis transmembrane conductance regulator. Structure and function of an epithelial chloride channel.Airway plumbing.Role of the cystic fibrosis transmembrane conductance regulator in innate immunity to Pseudomonas aeruginosa infections.Regulation of airway tight junctions by proinflammatory cytokines.Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infectionsCharacterization of the mouse beta defensin 1, Defb1, mutant mouse model.New approaches to cystic fibrosis.Development of PEGylated PLGA nanoparticle for controlled and sustained drug delivery in cystic fibrosisAirway surface liquid: end of the controversy?Is cystic fibrosis lung disease caused by abnormal ion composition or abnormal volume?Evaluation of thiol-based antioxidant therapeutics in cystic fibrosis sputum: Focus on myeloperoxidase.Mucus clearance as a primary innate defense mechanism for mammalian airways.Mucociliary clearance in cystic fibrosis.Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia.Rescuing protein conformation: prospects for pharmacological therapy in cystic fibrosisHuman cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.Phenotypic profiling of Scedosporium aurantiacum, an opportunistic pathogen colonizing human lungs.Progression of pulmonary hyperinflation and trapped gas associated with genetic and environmental factors in children with cystic fibrosis.RNA sequencing from human neutrophils reveals distinct transcriptional differences associated with chronic inflammatory states.Computed Tomography (CT) Scanning Facilitates Early Identification of Neonatal Cystic Fibrosis PigletsNoninvasive in vivo fluorescence measurement of airway-surface liquid depth, salt concentration, and pH.Pathogen-host interactions in Pseudomonas aeruginosa pneumoniaReduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung.Targeted Antibiotic Prophylaxis for Lung Transplantation in Cystic Fibrosis Patients Colonised with Pseudomonas aeruginosa Using Multiple Combination Bactericidal Testing.Long term effects of azithromycin in patients with cystic fibrosis: A double blind, placebo controlled trial.Soluble mediators, not cilia, determine airway surface liquid volume in normal and cystic fibrosis superficial airway epithelia.Airway surface liquid osmolality measured using fluorophore-encapsulated liposomes.
P2860
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P2860
description
1999 nî lūn-bûn
@nan
1999年の論文
@ja
1999年学术文章
@wuu
1999年学术文章
@zh-cn
1999年学术文章
@zh-hans
1999年学术文章
@zh-my
1999年学术文章
@zh-sg
1999年學術文章
@yue
1999年學術文章
@zh
1999年學術文章
@zh-hant
name
The genesis of cystic fibrosis lung disease.
@en
type
label
The genesis of cystic fibrosis lung disease.
@en
prefLabel
The genesis of cystic fibrosis lung disease.
@en
P2860
P356
P1476
The genesis of cystic fibrosis lung disease.
@en
P2093
P2860
P304
P356
10.1172/JCI6222
P407
P577
1999-02-01T00:00:00Z