Fibrillin-1: organization in microfibrils and structural properties.
about
The evolution of extracellular fibrillins and their functional domainsEvidence for a critical contribution of haploinsufficiency in the complex pathogenesis of Marfan syndromeSpecific sequence motif of 8-Cys repeats of TGF-beta binding proteins, LTBPs, creates a hydrophobic interaction surface for binding of small latent TGF-betaADAMTS10 protein interacts with fibrillin-1 and promotes its deposition in extracellular matrix of cultured fibroblasts.Heparin/heparan sulfate controls fibrillin-1, -2 and -3 self-interactions in microfibril assemblyThe membrane-spanning proteoglycan NG2 binds to collagens V and VI through the central nonglobular domain of its core proteinProlyl 3-hydroxylase 1, enzyme characterization and identification of a novel family of enzymesStructure of the integrin binding fragment from fibrillin-1 gives new insights into microfibril organizationDimer model for the microfibrillar protein fibulin-2 and identification of the connecting disulfide bridgePerforin-independent extracellular granzyme B activity contributes to abdominal aortic aneurysmFunctional consequences of homocysteinylation of the elastic fiber proteins fibrillin-1 and tropoelastinStructure and interdomain interactions of a hybrid domain: a disulphide-rich module of the fibrillin/LTBP superfamily of matrix proteinsThe molecular genetics of Marfan syndrome and related disordersFibrillin: from microfibril assembly to biomechanical functionThe molecular genetics of Marfan syndrome and related microfibrillopathiesRegulation of limb patterning by extracellular microfibrilsAbsence of autoantibodies against correctly folded recombinant fibrillin-1 protein in systemic sclerosis patientsCorneal stroma microfibrilsAbnormal Activation of BMP Signaling Causes Myopathy in Fbn2 Null MiceStructure of the Fibrillin-1 N-Terminal Domains Suggests that Heparan Sulfate Regulates the Early Stages of Microfibril AssemblyFibrillin-1 directly regulates osteoclast formation and function by a dual mechanismCharacterization of Microfibrillar-associated Protein 4 (MFAP4) as a Tropoelastin- and Fibrillin-binding Protein Involved in Elastic Fiber FormationSequence and expression of a novel member (LTBP-4) of the family of latent transforming growth factor-beta binding proteinsMAGP-2 has multiple binding regions on fibrillins and has covalent periodic association with fibrillin-containing microfibrilsTargeting of bone morphogenetic protein growth factor complexes to fibrillinCell adhesion to fibrillin-1 molecules and microfibrils is mediated by alpha 5 beta 1 and alpha v beta 3 integrinsInteractions of fibrillin-1 with heparin/heparan sulfate, implications for microfibrillar assemblyMolecular interactions of biglycan and decorin with elastic fiber components: biglycan forms a ternary complex with tropoelastin and microfibril-associated glycoprotein 1Protein interaction studies of MAGP-1 with tropoelastin and fibrillin-1Identification of a matrix-binding domain in MAGP1 and MAGP2 and intracellular localization of alternative splice formsMicrofibril-associated glycoprotein-1 (MAGP-1) binds to the pepsin-resistant domain of the alpha3(VI) chain of type VI collagenIdentification of a major microfibril-associated glycoprotein-1-binding domain in fibrillin-2Fibrillin-1 and fibulin-2 interact and are colocalized in some tissuesADAMTSL-6 is a novel extracellular matrix protein that binds to fibrillin-1 and promotes fibrillin-1 fibril formationFibrillin degradation by matrix metalloproteinases: implications for connective tissue remodellingIntracellular mechanisms of molecular recognition and sorting for transport of large extracellular matrix moleculesIn vivo studies of mutant fibrillin-1 microfibrilsMicrofibril-associated glycoprotein-2 interacts with fibrillin-1 and fibrillin-2 suggesting a role for MAGP-2 in elastic fiber assembly.The exon structure of the human MAGP-2 gene. Similarity with the MAGP-1 gene is confined to two exons encoding a cysteine-rich region.Biogenesis and function of fibrillin assemblies.
P2860
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P2860
Fibrillin-1: organization in microfibrils and structural properties.
description
1996 nî lūn-bûn
@nan
1996年の論文
@ja
1996年論文
@yue
1996年論文
@zh-hant
1996年論文
@zh-hk
1996年論文
@zh-mo
1996年論文
@zh-tw
1996年论文
@wuu
1996年论文
@zh
1996年论文
@zh-cn
name
Fibrillin-1: organization in microfibrils and structural properties.
@en
type
label
Fibrillin-1: organization in microfibrils and structural properties.
@en
prefLabel
Fibrillin-1: organization in microfibrils and structural properties.
@en
P2093
P356
P1476
Fibrillin-1: organization in microfibrils and structural properties.
@en
P2093
D P Reinhardt
G M Corson
H P Bächinger
J E Gambee
P304
P356
10.1006/JMBI.1996.0237
P407
P577
1996-04-01T00:00:00Z