Assessment of mitochondrial oxidative phosphorylation in patient muscle biopsies, lymphoblasts, and transmitochondrial cell lines.
about
Ancient mtDNA genetic variants modulate mtDNA transcription and replicationMitochondrial dysfunction and mitophagy activation in blood mononuclear cells of fibromyalgia patients: implications in the pathogenesis of the diseaseDiabetic cardiomyopathy-associated dysfunction in spatially distinct mitochondrial subpopulationsLate-onset Leigh syndrome in a patient with mitochondrial complex I NDUFS8 mutationsStructural organization of mitochondrial human complex I: role of the ND4 and ND5 mitochondria-encoded subunits and interaction with prohibitinMammalian polynucleotide phosphorylase is an intermembrane space RNase that maintains mitochondrial homeostasisPhosphate-activated glutaminase (GLS2), a p53-inducible regulator of glutamine metabolism and reactive oxygen speciesHuman ind1, an iron-sulfur cluster assembly factor for respiratory complex IRole of SUV3 helicase in maintaining mitochondrial homeostasis in human cellsMutations of human NARS2, encoding the mitochondrial asparaginyl-tRNA synthetase, cause nonsyndromic deafness and Leigh syndromeHsp27 as a negative regulator of cytochrome C release.A mutation of beta -actin that alters depolymerization dynamics is associated with autosomal dominant developmental malformations, deafness, and dystoniaMetabolic control analysis in a cellular model of elevated MAO-B: relevance to Parkinson's diseaseSarcalumenin is essential for maintaining cardiac function during endurance exercise trainingThe NDUFA1 gene product (MWFE protein) is essential for activity of complex I in mammalian mitochondriaTruncated product of the bifunctional DLST gene involved in biogenesis of the respiratory chainMitochondrial DNA variation in human radiation and diseaseMitochondrial genetics and obesity: evolutionary adaptation and contemporary disease susceptibilityMAO-B elevation in mouse brain astrocytes results in Parkinson's pathologyPostnatal proteasome inhibition induces neurodegeneration and cognitive deficiencies in adult mice: a new model of neurodevelopment syndromeSkeletal muscle mitochondrial health and spinal cord injuryMitochondrial ribosomal RNA (rRNA) methyltransferase family members are positioned to modify nascent rRNA in foci near the mitochondrial DNA nucleoidConditional knockdown of hMRS2 results in loss of mitochondrial Mg(2+) uptake and cell deathThe ADP/ATP translocator is not essential for the mitochondrial permeability transition poreSyndromic parkinsonism and dementia associated with OPA1 missense mutationsThe enzymatic function of tafazzinDeletion of skeletal muscle SOCS3 prevents insulin resistance in obesityA novel deletion in the GTPase domain of OPA1 causes defects in mitochondrial morphology and distribution, but not in functionTransmission and prenatal diagnosis of the T9176C mitochondrial DNA mutationMitochondrial toxin 3-nitropropionic acid induces cardiac and neurotoxicity differentially in miceMitochondrial dysfunction in the type 2 diabetic heart is associated with alterations in spatially distinct mitochondrial proteomesTransgenic overexpression of mitofilin attenuates diabetes mellitus-associated cardiac and mitochondria dysfunctionFunctional deficiencies of subsarcolemmal mitochondria in the type 2 diabetic human heartThe background of mitochondrial DNA haplogroup J increases the sensitivity of Leber's hereditary optic neuropathy cells to 2,5-hexanedione toxicityReversal of mitochondrial proteomic loss in Type 1 diabetic heart with overexpression of phospholipid hydroperoxide glutathione peroxidaseSuppression of oxidative stress by resveratrol after isometric contractions in gastrocnemius muscles of aged miceHeterozygous mutation of Drosophila Opa1 causes the development of multiple organ abnormalities in an age-dependent and organ-specific mannerMetabolic adaptation to chronic inhibition of mitochondrial protein synthesis in acute myeloid leukemia cellsMitochondrial disease in superoxide dismutase 2 mutant miceInhibition of cathepsin B by E-64 induces oxidative stress and apoptosis in filarial parasite
P2860
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P2860
Assessment of mitochondrial oxidative phosphorylation in patient muscle biopsies, lymphoblasts, and transmitochondrial cell lines.
description
1996 nî lūn-bûn
@nan
1996年の論文
@ja
1996年学术文章
@wuu
1996年学术文章
@zh-cn
1996年学术文章
@zh-hans
1996年学术文章
@zh-my
1996年学术文章
@zh-sg
1996年學術文章
@yue
1996年學術文章
@zh
1996年學術文章
@zh-hant
name
Assessment of mitochondrial ox ...... transmitochondrial cell lines.
@en
type
label
Assessment of mitochondrial ox ...... transmitochondrial cell lines.
@en
prefLabel
Assessment of mitochondrial ox ...... transmitochondrial cell lines.
@en
P2093
P921
P1476
Assessment of mitochondrial ox ...... transmitochondrial cell lines.
@en
P2093
P304
P356
10.1016/S0076-6879(96)64044-0
P407
P577
1996-01-01T00:00:00Z