Defective acidification of intracellular organelles in cystic fibrosis.
about
An endosomal beta COP is involved in the pH-dependent formation of transport vesicles destined for late endosomesMechanisms of lipid malabsorption in Cystic Fibrosis: the impact of essential fatty acids deficiencyAberrant autolysosomal regulation is linked to the induction of embryonic senescence: differential roles of Beclin 1 and p53 in vertebrate Spns1 deficiencyOntogeny of CLCN3 chloride channel gene expression in human pulmonary epitheliumHyperacidification of cellubrevin endocytic compartments and defective endosomal recycling in cystic fibrosis respiratory epithelial cellsCystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surfaceAltered cholesterol homeostasis in cultured and in vivo models of cystic fibrosisSubcellular localization of CFTR to endosomes in a ductal epitheliumMicrobial pathogenesis in cystic fibrosis: mucoid Pseudomonas aeruginosa and Burkholderia cepaciaDefective goblet cell exocytosis contributes to murine cystic fibrosis-associated intestinal disease.The voltage-dependent Cl(-) channel ClC-5 and plasma membrane Cl(-) conductances of mouse renal collecting duct cells (mIMCD-3).Mucin glycosylation and sulphation in airway epithelial cells is not influenced by cystic fibrosis transmembrane conductance regulator expression.Efficient gene transfer into human normal and cystic fibrosis tracheal gland serous cells with synthetic vectors.Terminal sialylation is altered in airway cells with impaired CFTR-mediated chloride transport.CFTR modulates programmed cell death by decreasing intracellular pH in Chinese hamster lung fibroblasts.Using polarization-shaped optical vortex traps for single-cell nanosurgery.Reduced GM1 ganglioside in CFTR-deficient human airway cells results in decreased β1-integrin signaling and delayed wound repairGene therapy for cystic fibrosis.TLR-4-mediated innate immunity is reduced in cystic fibrosis airway cells.Yet another role for the cystic fibrosis transmembrane conductance regulator.Inflammation and CFTR: might neutrophils be the key in cystic fibrosis?SNARE-dependent glutamate release in megakaryocytes.Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cellsFunctional vacuolar ATPase (V-ATPase) proton pumps traffic to the enterocyte brush border membrane and require CFTR.Molecular basis for defective glycosylation and Pseudomonas pathogenesis in cystic fibrosis lung.Role of the cystic fibrosis transmembrane conductance regulator in innate immunity to Pseudomonas aeruginosa infections.The cystic fibrosis transmembrane regulator (CFTR) in the kidney.Chloride channels of intracellular membranesModifications of glycans: biological significance and therapeutic opportunitiesLinkage of azurophil granule secretion in neutrophils to chloride ion transport and endosomal transcytosis.Localization of cystic fibrosis transmembrane conductance regulator mRNA in the human gastrointestinal tract by in situ hybridization.A new role for bicarbonate in mucus formation.Severe deficiency of cystic fibrosis transmembrane conductance regulator messenger RNA carrying nonsense mutations R553X and W1316X in respiratory epithelial cells of patients with cystic fibrosis.The pH of the secretory pathway: measurement, determinants, and regulation.Sphingoid long chain bases prevent lung infection by Pseudomonas aeruginosa.Renal vacuolar H+-ATPase.Conditions associated with the cystic fibrosis defect promote chronic Pseudomonas aeruginosa infectionBiosynthesis and secretion of pituitary hormones: dynamics and regulation.Endosomal hyperacidification in cystic fibrosis is due to defective nitric oxide-cylic GMP signalling cascadeAsialo GM1 is a receptor for Pseudomonas aeruginosa adherence to regenerating respiratory epithelial cells
P2860
Q24671983-4FB1B504-4C3B-4D7F-8AE0-B26532C8339CQ24806288-0E24E7AD-4084-442E-BEA9-FDCACCA75947Q27315143-217A32FA-6386-470B-A1CC-4B85FEFF144EQ28212863-27E01698-D72B-4C11-9611-634B9D65125CQ28216541-CE248503-0EA8-47CE-9A2A-337AE04092E7Q28368071-C6B03C58-3AE5-4F86-A231-DA78B9AAA6C2Q28509055-C1A719BE-002F-4EEE-A025-C6A73589A8D6Q28573599-5159D9FB-F355-4530-BD22-4A96DAA3E8F3Q29615286-3FBC9632-9F13-4495-A099-99A34B4691FDQ30628431-A941B885-A20D-4F95-9A0A-8CAD144C7262Q30760886-69844227-10A8-4F52-8674-018C63C7C5ECQ31144471-3FBD5990-1F7F-4D0C-82A2-F621415FA442Q31484629-44D4C8EB-253B-4240-BDA3-D94B8A21B0B4Q31834361-AB7EC8C5-FEA8-477A-A069-AB73EC818F48Q33182329-9A9D7FDF-24AD-42EB-9077-A8A1CBE1C7C4Q33273584-5721655A-6ABD-4DA1-8361-BA61091EE4B6Q33569399-970D870C-D5BA-4322-8E14-1FAC37364804Q33623207-EB9F4B72-66EE-4231-A8E4-4B949C0FF614Q33765010-C56FA125-1FB4-4A89-8F2D-CBBAA4318443Q33806101-F2A3290E-E1FB-4D20-AAC4-FAFE5DB39EC8Q33855072-01B85B74-F938-4009-909B-CDBE08BDB035Q33882687-BBE39797-FF26-4EA8-828C-D13D4B0A9F69Q33905211-67DEB20A-54B6-48AA-BAF0-1398551C27DDQ33944537-CD5E46A7-BBA8-45C1-A058-E69CC7B252CBQ33950252-60D97DA7-985D-44ED-BF1C-3C53935961BEQ33988505-498B7B24-55F3-4883-92A9-F0D52590B9CAQ34058054-BD6B1D84-3519-40FC-83F9-CB01A4B75922Q34091107-0FF1CB44-7C90-475A-AB33-E43B7447629EQ34111293-A898F2F3-B069-4C93-98AD-CFED0497FA03Q34119970-8208B1A1-DB74-4C48-B5DC-44CD07079CC2Q34120803-597243A2-288C-4E0D-85CA-F1E9C17DB363Q34212678-5B66F00C-D808-4F16-8C64-10015F0A2121Q34213495-71634023-E31D-4600-B0A1-66BEF54E9520Q34340217-92495722-65C8-4D79-B0DB-33AC4292B77BQ34342508-F4C6DAF1-5CE3-44A3-BB71-34BEAC307FA8Q34350645-04C7C3D4-3E38-4BC9-892B-D5E47671D878Q34479389-E5C51DE0-A357-44E1-8C1C-7C78B641F04DQ34589298-4339E30E-44FF-4C89-AD6C-B7DB0E669E78Q34683157-62E81995-751D-4AED-AAEF-698EF1507A3DQ34732927-95CA9DAB-7CF9-4F37-9A63-91DC92D8713F
P2860
Defective acidification of intracellular organelles in cystic fibrosis.
description
1991 nî lūn-bûn
@nan
1991年の論文
@ja
1991年論文
@yue
1991年論文
@zh-hant
1991年論文
@zh-hk
1991年論文
@zh-mo
1991年論文
@zh-tw
1991年论文
@wuu
1991年论文
@zh
1991年论文
@zh-cn
name
Defective acidification of intracellular organelles in cystic fibrosis.
@en
type
label
Defective acidification of intracellular organelles in cystic fibrosis.
@en
prefLabel
Defective acidification of intracellular organelles in cystic fibrosis.
@en
P2093
P356
P1433
P1476
Defective acidification of intracellular organelles in cystic fibrosis.
@en
P2093
P2888
P356
10.1038/352070A0
P407
P577
1991-07-01T00:00:00Z
P5875
P6179
1005939502