Chemical chaperone TUDCA preserves cone photoreceptors in a mouse model of Leber congenital amaurosis.
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Natural Compounds from Saffron and Bear Bile Prevent Vision Loss and Retinal DegenerationThe Unexpected Uses of Urso- and Tauroursodeoxycholic Acid in the Treatment of Non-liver DiseasesBile Acids in Neurodegenerative DisordersRestoration of mutant bestrophin-1 expression, localisation and function in a polarised epithelial cell modelPharmacological Amelioration of Cone Survival and Vision in a Mouse Model for Leber Congenital AmaurosisPathophysilogical mechanism and treatment strategies for Leber congenital amaurosis.Endoplasmic reticulum stress and the unfolded protein responses in retinal degeneration.Retinal degeneration in animal models with a defective visual cycle.QLT091001, a 9-cis-retinal analog, is well-tolerated by retinas of mice with impaired visual cycles.Retinal cone photoreceptors require phosducin-like protein 1 for G protein complex assembly and signalingGenetic deletion of S-opsin prevents rapid cone degeneration in a mouse model of Leber congenital amaurosisNeuroprotective Effect of Tauroursodeoxycholic Acid on N-Methyl-D-Aspartate-Induced Retinal Ganglion Cell Degeneration.Controlled delivery of tauroursodeoxycholic acid from biodegradable microspheres slows retinal degeneration and vision loss in P23H rats.Neuronatin is a stress-responsive protein of rod photoreceptors.Vitamin A derivatives as treatment options for retinal degenerative diseases.A review of therapeutic prospects of non-viral gene therapy in the retinal pigment epitheliumLoss of cone cyclic nucleotide-gated channel leads to alterations in light response modulating system and cellular stress response pathways: a gene expression profiling study.Mosaic synaptopathy and functional defects in Cav1.4 heterozygous mice and human carriers of CSNB2.Leber's Congenital Amaurosis and Gene Therapy.The molecular and cellular basis of rhodopsin retinitis pigmentosa reveals potential strategies for therapy.Patients and animal models of CNGβ1-deficient retinitis pigmentosa support gene augmentation approach.Gene therapy restores vision and delays degeneration in the CNGB1(-/-) mouse model of retinitis pigmentosa.Endoplasmic reticulum (ER) Ca2+-channel activity contributes to ER stress and cone death in cyclic nucleotide-gated channel deficiency.Neuroprotective strategies for retinal disease.
P2860
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P2860
Chemical chaperone TUDCA preserves cone photoreceptors in a mouse model of Leber congenital amaurosis.
description
2012 nî lūn-bûn
@nan
2012年の論文
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2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
2012年论文
@zh
2012年论文
@zh-cn
name
Chemical chaperone TUDCA prese ...... of Leber congenital amaurosis.
@en
type
label
Chemical chaperone TUDCA prese ...... of Leber congenital amaurosis.
@en
prefLabel
Chemical chaperone TUDCA prese ...... of Leber congenital amaurosis.
@en
P2093
P2860
P921
P356
P1476
Chemical chaperone TUDCA prese ...... of Leber congenital amaurosis.
@en
P2093
Wolfgang Baehr
Yingbin Fu
P2860
P304
P356
10.1167/IOVS.12-9851
P407
P577
2012-06-05T00:00:00Z