Substrate Deprivation Therapy to Reduce Glycosaminoglycan Synthesis Improves Aspects of Neurological and Skeletal Pathology in MPS I Mice.

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Substrate Deprivation Therapy to Reduce Glycosaminoglycan Synthesis Improves Aspects of Neurological and Skeletal Pathology in MPS I Mice.

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2017 nî lūn-bûn

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2017年の論文

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2017年論文

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2017年論文

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2017年論文

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2017年論文

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2017年論文

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2017年论文

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2017年论文

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Substrate Deprivation Therapy ...... letal Pathology in MPS I Mice.

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Substrate Deprivation Therapy ...... letal Pathology in MPS I Mice.

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Substrate Deprivation Therapy ...... letal Pathology in MPS I Mice.

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P1476

Substrate Deprivation Therapy ...... letal Pathology in MPS I Mice.

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P2093

Ainslie L K Derrick-Roberts

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Carmen E Pyragius

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P2860

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Genistein improves neuropathology and corrects behaviour in a mouse model of neurodegenerative metabolic disease

Rhodamine B ingestion as a cause of fluorescent red urine

Prevalence of lysosomal storage disorders.

Characterization of an immunodeficient mouse model of mucopolysaccharidosis type I suitable for preclinical testing of human stem cell and gene therapy.

Genistein reduces lysosomal storage in peripheral tissues of mucopolysaccharide IIIB mice.

P31

scholarly article

P356

10.3390/DISEASES5010005

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P433

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Matilda Jackson

S Byers

P577

2017-02-23T00:00:00Z

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28933358

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5456338

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