Rough endoplasmic reticulum trafficking errors by different classes of mutant dentin sialophosphoprotein (DSPP) cause dominant negative effects in both dentinogenesis imperfecta and dentin dysplasia by entrapping normal DSPP.
about
Intrinsically disordered proteins and biomineralization.Immunolocalization of skeletal matrix proteins in tissue and mineral of the coral Stylophora pistillataDspp mutations disrupt mineralization homeostasis during odontoblast differentiation.The dentin phosphoprotein repeat region and inherited defects of dentin.A DSPP mutation causing dentinogenesis imperfecta and characterization of the mutational effect.Transgenic expression of dentin phosphoprotein inhibits skeletal development.N-terminal Dentin Sialoprotein fragment induces type I collagen production and upregulates dentinogenesis marker expression in osteoblasts.Deletion of amelotin exons 3-6 is associated with amelogenesis imperfecta.The role of acidic phosphoproteins in biomineralization.The LPV Motif Is Essential for the Efficient Export of Secretory DMP1 From the Endoplasmic Reticulum.Accelerated enamel mineralization in Dspp mutant mice.Phenotype and genotype analyses in seven families with dentinogenesis imperfecta or dentin dysplasia.Efficient trafficking of acidic proteins out of the endoplasmic reticulum involves a conserved amino terminal IleProVal (IPV)-like tripeptide motif.Reduced Dentin Matrix Protein Expression in Camurati-Engelmann Disease Transgenic Mouse Model.Surf4 (Erv29p) binds amino-terminal tripeptide motifs of soluble cargo proteins with different affinities, enabling prioritization of their exit from the endoplasmic reticulum
P2860
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P2860
Rough endoplasmic reticulum trafficking errors by different classes of mutant dentin sialophosphoprotein (DSPP) cause dominant negative effects in both dentinogenesis imperfecta and dentin dysplasia by entrapping normal DSPP.
description
2012 nî lūn-bûn
@nan
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
2012年论文
@zh
2012年论文
@zh-cn
name
Rough endoplasmic reticulum tr ...... sia by entrapping normal DSPP.
@en
Rough endoplasmic reticulum tr ...... ant dentin sialophosphoprotein
@nl
type
label
Rough endoplasmic reticulum tr ...... sia by entrapping normal DSPP.
@en
Rough endoplasmic reticulum tr ...... ant dentin sialophosphoprotein
@nl
prefLabel
Rough endoplasmic reticulum tr ...... sia by entrapping normal DSPP.
@en
Rough endoplasmic reticulum tr ...... ant dentin sialophosphoprotein
@nl
P2093
P2860
P356
P1476
Rough endoplasmic reticulum tr ...... sia by entrapping normal DSPP.
@en
P2093
Dianalee A McKnight
Larry W Fisher
Matthew D Phillips
Zofia von Marschall
P2860
P304
P356
10.1002/JBMR.1573
P577
2012-06-01T00:00:00Z