Glycogen metabolism in tissues from a mouse model of Lafora disease.
about
A role for AGL ubiquitination in the glycogen storage disorders of Lafora and Cori's diseaseMalin decreases glycogen accumulation by promoting the degradation of protein targeting to glycogen (PTG)Laforin is a glycogen phosphatase, deficiency of which leads to elevated phosphorylation of glycogen in vivo.Co-chaperone CHIP stabilizes aggregate-prone malin, a ubiquitin ligase mutated in Lafora disease.Abnormal glycogen chain length pattern, not hyperphosphorylation, is critical in Lafora disease.Genetic depletion of the malin E3 ubiquitin ligase in mice leads to lafora bodies and the accumulation of insoluble laforinRefeeding-induced brown adipose tissue glycogen hyper-accumulation in mice is mediated by insulin and catecholaminesLaforin, a protein with many faces: glucan phosphatase, adapter protein, et alii.Protein tyrosine phosphatases: dual-specificity phosphatases in health and disease.Glycogen and its metabolism: some new developments and old themes.Epilepsy, regulation of brain energy metabolism and neurotransmission.Analysis of flurothyl-induced myoclonus in inbred strains of mice.Lafora disease: insights into neurodegeneration from plant metabolism.The regulation of muscle glycogen: the granule and its proteins.Regulation of glycogen synthesis by the laforin-malin complex is modulated by the AMP-activated protein kinase pathway.Lafora disease proteins malin and laforin are recruited to aggresomes in response to proteasomal impairment.Abnormal metabolism of glycogen phosphate as a cause for Lafora disease.Suppression of leptin signaling reduces polyglucosan inclusions and seizure susceptibility in a mouse model for Lafora disease.Glycogen as a Putative Target for Diagnosis and Therapy in Brain Pathologies
P2860
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P2860
Glycogen metabolism in tissues from a mouse model of Lafora disease.
description
2006 nî lūn-bûn
@nan
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
2006年论文
@zh
2006年论文
@zh-cn
name
Glycogen metabolism in tissues from a mouse model of Lafora disease.
@en
Glycogen metabolism in tissues from a mouse model of Lafora disease.
@nl
type
label
Glycogen metabolism in tissues from a mouse model of Lafora disease.
@en
Glycogen metabolism in tissues from a mouse model of Lafora disease.
@nl
prefLabel
Glycogen metabolism in tissues from a mouse model of Lafora disease.
@en
Glycogen metabolism in tissues from a mouse model of Lafora disease.
@nl
P2093
P2860
P1476
Glycogen metabolism in tissues from a mouse model of Lafora disease.
@en
P2093
Alexander V Skurat
Anna A DePaoli-Roach
Berge A Minassian
Peter J Roach
P2860
P304
P356
10.1016/J.ABB.2006.10.017
P407
P50
P577
2006-11-03T00:00:00Z