Impaired clearance of free cystine from lysosome-enriched granular fractions of I-cell-disease fibroblasts.

about

Iron in cytosolic ferritin can be recycled through lysosomal degradation in human fibroblasts.

P2860

Q41814987-B4A1A243-AAF5-421A-BD48-4FD4550E3C04

P2860

Impaired clearance of free cystine from lysosome-enriched granular fractions of I-cell-disease fibroblasts.

Item

http://www.wikidata.org/entity/Q42854024

description

1986 nî lūn-bûn

@nan

1986年の論文

@ja

1986年論文

@yue

1986年論文

@zh-hant

1986年論文

@zh-hk

1986年論文

@zh-mo

1986年論文

@zh-tw

1986年论文

@wuu

1986年论文

@zh

1986年论文

@zh-cn

name

Impaired clearance of free cys ...... of I-cell-disease fibroblasts.

@en

Impaired clearance of free cys ...... of I-cell-disease fibroblasts.

@nl

type

Item

label

Impaired clearance of free cys ...... of I-cell-disease fibroblasts.

@en

Impaired clearance of free cys ...... of I-cell-disease fibroblasts.

@nl

prefLabel

Impaired clearance of free cys ...... of I-cell-disease fibroblasts.

@en

Impaired clearance of free cys ...... of I-cell-disease fibroblasts.

@nl

P1476

Impaired clearance of free cys ...... of I-cell-disease fibroblasts.

@en

P2093

F Tietze

http://www.w3.org/2001/XMLSchema#string

G S Harper

http://www.w3.org/2001/XMLSchema#string

J D Butler

http://www.w3.org/2001/XMLSchema#string

L H Rome

http://www.w3.org/2001/XMLSchema#string

W A Gahl

http://www.w3.org/2001/XMLSchema#string

P2860

Protein measurement with the Folin phenol reagent

Cystine transport is defective in isolated leukocyte lysosomes from patients with cystinosis

UDP-N-acetylglucosamine:glycoprotein N-acetylglucosamine-1-phosphotransferase. Proposed enzyme for the phosphorylation of the high mannose oligosaccharide units of lysosomal enzymes

Lysosomal enzyme targeting. N-Acetylglucosaminylphosphotransferase selectively phosphorylates native lysosomal enzymes

Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts.

Lysosomal cystine counter-transport in heterozygotes for cystinosis.

Cystine accumulation and clearance by normal and cystinotic leukocytes exposed to cystine dimethyl ester.

Fibroblasts from patients with I-cell disease and pseudo-Hurler polydystrophy are deficient in uridine 5'-diphosphate-N-acetylglucosamine: glycoprotein N-acetylglucosaminylphosphotransferase activity.

Enzymic diagnosis of the genetic mucopolysaccharide storage disorders.

The phosphomannosyl recognition system for intracellular and intercellular transport of lysosomal enzymes.

P304

9-15

http://www.w3.org/2001/XMLSchema#string

P31

scholarly article

P356

10.1042/BJ2370009

http://www.w3.org/2001/XMLSchema#string

P407

English

P433

http://www.w3.org/2001/XMLSchema#string

P478

237

http://www.w3.org/2001/XMLSchema#string

P577

1986-07-01T00:00:00Z

http://www.w3.org/2001/XMLSchema#dateTime

P5875

19360828

http://www.w3.org/2001/XMLSchema#string

P698

3800891

http://www.w3.org/2001/XMLSchema#string

P932

1146941

http://www.w3.org/2001/XMLSchema#string

Impaired clearance of free cystine from lysosome-enriched granular fractions of I-cell-disease fibroblasts.

about

P2860

P2860

Impaired clearance of free cystine from lysosome-enriched granular fractions of I-cell-disease fibroblasts.

description

name

type

label

prefLabel

P1433

P1476

P2093

P2860

P304

P31

P356

P407

P433

P478

P577

P5875

P698

P932

P356

P1433

P1476

P2093

P2860

P304

P31

P356

P407

P433

P478

P577

P5875

P698

P932