Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
about
Interstitial lung disease in children -- genetic background and associated phenotypes.Expression profiles of hydrophobic surfactant proteins in children with diffuse chronic lung disease.Maternal synchronization of gestational length and lung maturationGenetic disorders of surfactant dysfunctionInduction and apoptotic regression of lung adenocarcinomas by regulation of a K-Ras transgene in the presence and absence of tumor suppressor genesKGF regulates pulmonary epithelial proliferation and surfactant protein gene expression in adult rat lungSP-B and SP-C containing new synthetic surfactant for treatment of extremely immature lamb lungSurfactant protein SP-B strongly modifies surface collapse of phospholipid vesicles: insights from a quartz crystal microbalance with dissipation.Nedd4-2-mediated ubiquitination facilitates processing of surfactant protein-CPulmonary malformation in transgenic mice expressing human keratinocyte growth factor in the lung.Conditional deletion of Abca3 in alveolar type II cells alters surfactant homeostasis in newborn and adult mice.Targeted disruption of the surfactant protein B gene disrupts surfactant homeostasis, causing respiratory failure in newborn mice.Diseases of pulmonary surfactant homeostasis.Cryopreservation and in vitro culture of primary cell types from lung tissue of a stranded pygmy sperm whale (Kogia breviceps).Adaptation and increased susceptibility to infection associated with constitutive expression of misfolded SP-C.Clinical and ultrastructural spectrum of diffuse lung disease associated with surfactant protein C mutations.LPS-treated macrophage cytokines repress surfactant protein-B in lung epithelial cells.Altered surfactant function and structure in SP-A gene targeted mice.An overview of pulmonary surfactant in the neonate: genetics, metabolism, and the role of surfactant in health and disease.Pulmonary surfactant: an immunological perspective.Mature Surfactant Protein-B Expression by Immunohistochemistry as a Marker for Surfactant System Development in the Fetal Sheep LungHypoxia up-regulates expression of hemoglobin in alveolar epithelial cells.Thrombospondin-1 is required for normal murine pulmonary homeostasis and its absence causes pneumonia.Hepatocyte nuclear factor 3 activates transcription of thyroid transcription factor 1 in respiratory epithelial cellsFormation of three-dimensional protein-lipid aggregates in monolayer films induced by surfactant protein B.Multilayer structures in lipid monolayer films containing surfactant protein C: effects of cholesterol and POPE.Reverse-phase HPLC of the hydrophobic pulmonary surfactant proteins: detection of a surfactant protein C isoform containing Nepsilon-palmitoyl-lysine.Antisense inhibition of surfactant protein A decreases tubular myelin formation in human fetal lung in vitro.Maintenance of the mouse type II cell phenotype in vitro.Defective pro-SFTPB causes pulmonary surfactant metabolism dysfunction 1 (SMDP1) and respiratory distress syndrome (RDS)SP-B deficiency causes respiratory failure in adult mice.Regulation of surfactant proteins by LPS and proinflammatory cytokines in fetal and newborn lung.cDNA cloning of ovine pulmonary SP-A, SP-B, and SP-C: isolation of two different sequences for SP-B.Genetic Association of Pulmonary Surfactant Protein Genes, SFTPA1, SFTPA2, SFTPB, SFTPC, and SFTPD With Cystic Fibrosis
P2860
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P2860
Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
description
1995 nî lūn-bûn
@nan
1995年の論文
@ja
1995年学术文章
@wuu
1995年学术文章
@zh
1995年学术文章
@zh-cn
1995年学术文章
@zh-hans
1995年学术文章
@zh-my
1995年学术文章
@zh-sg
1995年學術文章
@yue
1995年學術文章
@zh-hant
name
Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
@en
Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
@nl
type
label
Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
@en
Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
@nl
prefLabel
Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
@en
Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
@nl
P2093
P1476
Aberrant processing of surfactant protein C in hereditary SP-B deficiency.
@en
P2093
Profitt SA
Vorbroker DK
Whitsett JA
P304
P356
10.1152/AJPLUNG.1995.268.4.L647
P407
P433
P577
1995-04-01T00:00:00Z