Classification of rare bleeding disorders (RBDs) based on the association between coagulant factor activity and clinical bleeding severity.
about
Treatment for preventing bleeding in people with haemophilia or other congenital bleeding disorders undergoing surgeryRare bleeding disorders - bleeding assessment tools, laboratory aspects and phenotype and therapy of FXI deficiencyClinical use and the Italian demand for activated prothrombin complex and activated recombinant factor VII concentratesCoagulation Factor XIIIA Subunit Missense Mutations Affect Structure and Function at the Various Steps of Factor XIII ActionDiagnosis, clinical manifestations and management of rare bleeding disorders in Iran.Rare coagulation factor deficiencies: a countrywide screening data from India.Abnormal plasma clot structure and stability distinguish bleeding risk in patients with severe factor XI deficiency.Gynaecological and obstetrical bleeding in women with factor XI deficiency - a systematic review.A case of factor X deficiency in a Chihuahua dogAutosomal recessive inherited bleeding disorders in Pakistan: a cross-sectional study from selected regions.Use of global assays to understand clinical phenotype in congenital factor VII deficiency.Restoring hemostasis: fibrinogen concentrate versus cryoprecipitate.Ongoing risk of thrombosis with factor XI concentrate: 5 years experience in two centres.Detection of mild inherited disorders of blood coagulation: current options and personal recommendations.A diagnostic approach to mild bleeding disorders.Congenital afibrinogenemia: from etiopathogenesis to challenging clinical management.Advances in the treatment of bleeding disorders.In vitro secretion deficits are common among human coagulation factor XIII subunit B missense mutants: correlations with patient phenotypes and molecular models.Eight novel F13A1 gene missense mutations in patients with mild FXIII deficiency: in silico analysis suggests changes in FXIII-A subunit structure/function.Frequency of the p.Gly262Asp mutation in congenital Factor X deficiency.Long-term prophylaxis in severe factor VII deficiency.Spontaneous thrombosis in a patient with factor XI deficiency homozygous for the p.Cys398Tyr mutation.Third trimester amniocentesis for diagnosis of inherited bleeding disorders prior to delivery.Factor VII assay performance: an analysis of the North American Specialized Coagulation Laboratory Association proficiency testing results.FXI concentrate use and risk of thrombosis.Bleeding phenotype and correlation with factor XI (FXI) activity in congenital FXI deficiency: results of a retrospective study from a single centre.Management of surgical procedures in children with severe FV deficiency: experience of 13 surgeries.Reduced fibrinolytic resistance in patients with factor XI deficiency. Evidence of a thrombin-independent impairment of the thrombin-activatable fibrinolysis inhibitor pathway.A large case series on surgical outcomes in congenital factor XIII deficiency patients in Iran.Pharmacokinetics of recombinant factor XIII at steady state in patients with congenital factor XIII A-subunit deficiency.Molecular genetic analysis of the F11 gene in 14 Turkish patients with factor XI deficiency: identification of novel and recurrent mutations and their inheritance within families.Factor X heterozygous mutation in a patient with potential risk of bleeding: A case report.Rare congenital bleeding disordersIdentification and characterization of novel mutations implicated in congenital fibrinogen disorders
P2860
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P2860
Classification of rare bleeding disorders (RBDs) based on the association between coagulant factor activity and clinical bleeding severity.
description
2012 nî lūn-bûn
@nan
2012年の論文
@ja
2012年学术文章
@wuu
2012年学术文章
@zh-cn
2012年学术文章
@zh-hans
2012年学术文章
@zh-my
2012年学术文章
@zh-sg
2012年學術文章
@yue
2012年學術文章
@zh
2012年學術文章
@zh-hant
name
Classification of rare bleedin ...... nd clinical bleeding severity.
@en
Classification of rare bleeding disorders
@nl
type
label
Classification of rare bleedin ...... nd clinical bleeding severity.
@en
Classification of rare bleeding disorders
@nl
prefLabel
Classification of rare bleedin ...... nd clinical bleeding severity.
@en
Classification of rare bleeding disorders
@nl
P2093
P2860
P1476
Classification of rare bleedin ...... nd clinical bleeding severity.
@en
P2093
A Srivastava
D Di Michele
P H B Bolton-Maggs
Project on Consensus Definitio ...... on Thrombosis and Haemostasis
P2860
P304
P356
10.1111/J.1538-7836.2012.04844.X
P577
2012-09-01T00:00:00Z