Physiological basis of cystic fibrosis: a historical perspective.
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Origins of cystic fibrosis lung diseaseCFTR in cystic fibrosis and cholera: from membrane transport to clinical practiceRole of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosisCFTR-deficient pigs display peripheral nervous system defects at birth.Assessing mucociliary transport of single particles in vivo shows variable speed and preference for the ventral trachea in newborn pigscAMP-independent phosphorylation activation of CFTR by G proteins in native human sweat duct.Cystic fibrosis: exploiting its genetic basis in the hunt for new therapiesPathology of gastrointestinal organs in a porcine model of cystic fibrosis.Non-specific activation of the epithelial sodium channel by the CFTR chloride channelChloride channels: often enigmatic, rarely predictable.Native small airways secrete bicarbonate.Elevated incidence of dental caries in a mouse model of cystic fibrosis.Electrophysiological evidence for the presence of cystic fibrosis transmembrane conductance regulator (CFTR) in mouse sperm.Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth.CFTR inhibition provokes an inflammatory response associated with an imbalance of the annexin A1 pathway.Structural and biophysical properties of a synthetic channel-forming peptide: designing a clinically relevant anion selective pore.Targeted ablation of the abcc6 gene results in ectopic mineralization of connective tissuesClara cell impact in air-side activation of CFTR in small pulmonary airwaysA molecular mechanism for aberrant CFTR-dependent HCO(3)(-) transport in cystic fibrosis.A new role for bicarbonate in mucus formation.CFTR-mediated Cl(-) transport in the acinar and duct cells of rabbit lacrimal gland.Syntaxin 16 binds to cystic fibrosis transmembrane conductance regulator and regulates its membrane trafficking in epithelial cells.Is cystic fibrosis lung disease caused by abnormal ion composition or abnormal volume?CFTR interacts with ZO-1 to regulate tight junction assembly and epithelial differentiation through the ZONAB pathway.Co action of CFTR and AQP1 increases permeability of peritoneal epithelial cells on estrogen-induced ovarian hyper stimulation syndrome.Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia.Soluble adenylyl cyclase in health and disease.Corticosteroids correct aberrant CFTR localization in the duct and regenerate acinar cells in autoimmune pancreatitis.Protection of Cftr knockout mice from acute lung infection by a helper-dependent adenoviral vector expressing Cftr in airway epithelia.Human cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.A fluid secretion pathway unmasked by acinar-specific Tmem16A gene ablation in the adult mouse salivary glandAnimal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology.Ae4 (Slc4a9) Anion Exchanger Drives Cl- Uptake-dependent Fluid Secretion by Mouse Submandibular Gland Acinar Cells.Liquid secretion properties of airway submucosal glands.Severe defects in absorptive ion transport in distal colons of mice that lack ClC-2 channels.Identification of a Cryptic Bacterial Promoter in Mouse (mdr1a) P-Glycoprotein cDNA.Defective regulatory volume decrease in human cystic fibrosis tracheal cells because of altered regulation of intermediate conductance Ca2+-dependent potassium channelsInhaled hypertonic saline in adults hospitalised for exacerbation of cystic fibrosis lung disease: a retrospective study.Targeted Antibiotic Prophylaxis for Lung Transplantation in Cystic Fibrosis Patients Colonised with Pseudomonas aeruginosa Using Multiple Combination Bactericidal Testing.ATP release via anion channels.
P2860
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P2860
Physiological basis of cystic fibrosis: a historical perspective.
description
1999 nî lūn-bûn
@nan
1999年の論文
@ja
1999年学术文章
@wuu
1999年学术文章
@zh-cn
1999年学术文章
@zh-hans
1999年学术文章
@zh-my
1999年学术文章
@zh-sg
1999年學術文章
@yue
1999年學術文章
@zh
1999年學術文章
@zh-hant
name
Physiological basis of cystic fibrosis: a historical perspective.
@en
Physiological basis of cystic fibrosis: a historical perspective.
@nl
type
label
Physiological basis of cystic fibrosis: a historical perspective.
@en
Physiological basis of cystic fibrosis: a historical perspective.
@nl
prefLabel
Physiological basis of cystic fibrosis: a historical perspective.
@en
Physiological basis of cystic fibrosis: a historical perspective.
@nl
P2860
P1476
Physiological basis of cystic fibrosis: a historical perspective.
@en
P2093
P M Quinton
P2860
P304
P356
10.1152/PHYSREV.1999.79.1.S3
P433
P577
1999-01-01T00:00:00Z