Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
about
Tissue-specific strategies of the very-long chain acyl-CoA dehydrogenase-deficient (VLCAD-/-) mouse to compensate a defective fatty acid β-oxidationMitochondrial dysfunction in fatty acid oxidation disorders: insights from human and animal studiesProlonged QTc interval in association with medium-chain acyl-coenzyme A dehydrogenase deficiencyMitochondrial fatty acid oxidation disorders: pathophysiological studies in mouse modelsProlonged QT interval and lipid alterations beyond β-oxidation in very long-chain acyl-CoA dehydrogenase null mouse hearts.A Delphi clinical practice protocol for the management of very long chain acyl-CoA dehydrogenase deficiencyLong-term correction of very long-chain acyl-coA dehydrogenase deficiency in mice using AAV9 gene therapy.Carnitine supplementation induces acylcarnitine production in tissues of very long-chain acyl-CoA dehydrogenase-deficient mice, without replenishing low free carnitine.Renal response to short- and long-term exercise in very-long-chain acyl-CoA dehydrogenase-deficient (VLCAD(-/-)) mice.Corresponding increase in long-chain acyl-CoA and acylcarnitine after exercise in muscle from VLCAD mice.Resistance to high-fat diet-induced obesity and insulin resistance in mice with very long-chain acyl-CoA dehydrogenase deficiency.Mitochondrial fatty acid biosynthesis and muscle fibre plasticity in very long-chain acyl-CoA dehydrogenase-deficient mice.Experimental evidence for protein oxidative damage and altered antioxidant defense in patients with medium-chain acyl-CoA dehydrogenase deficiency.
P2860
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P2860
Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年学术文章
@wuu
2005年学术文章
@zh-cn
2005年学术文章
@zh-hans
2005年学术文章
@zh-my
2005年学术文章
@zh-sg
2005年學術文章
@yue
2005年學術文章
@zh
2005年學術文章
@zh-hant
name
Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
@en
Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
@nl
type
label
Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
@en
Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
@nl
prefLabel
Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
@en
Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
@nl
P2093
P2860
P1433
P1476
Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice.
@en
P2093
Arnold W Strauss
Chonan Tokunaga
Ertan Mayatepek
Frederic M Vaz
Frits A Wijburg
Henk Overmars
Lodewijk Ijlst
Marinus Duran
Naomi van Vlies
Ronald J Wanders
P2860
P304
P356
10.1203/01.PDR.0000157915.26049.47
P407
P577
2005-03-17T00:00:00Z
P5875
P6179
1041736824