Amino-acid depletion induced by abnormal amino-acid conjugation and protein restriction in isovaleric acidemia.

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Dietary practices in isovaleric acidemia: A European survey.An overview of a cohort of South African patients with mitochondrial disorders.

P2860

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Amino-acid depletion induced by abnormal amino-acid conjugation and protein restriction in isovaleric acidemia.

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http://www.wikidata.org/entity/Q46675699

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2007 nî lūn-bûn

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2007年の論文

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2007年学术文章

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2007年学术文章

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2007年学术文章

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2007年学术文章

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2007年学术文章

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2007年学术文章

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2007年學術文章

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2007年學術文章

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name

Amino-acid depletion induced b ...... iction in isovaleric acidemia.

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Amino-acid depletion induced b ...... iction in isovaleric acidemia.

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Item

label

Amino-acid depletion induced b ...... iction in isovaleric acidemia.

@en

Amino-acid depletion induced b ...... iction in isovaleric acidemia.

@nl

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Amino-acid depletion induced b ...... iction in isovaleric acidemia.

@en

Amino-acid depletion induced b ...... iction in isovaleric acidemia.

@nl

P1476

Amino-acid depletion induced b ...... iction in isovaleric acidemia.

@en

P2093

Erasmus E

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Loots DT

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Mienie LJ

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P2860

The utilization of alanine, glutamic acid, and serine as amino acid substrates for glycine N-acyltransferase

Leucine supplementation and intensive training

Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia.

N-Isovalerylalanine and N-isovalerylsarcosine: two new minor metabolites in isovaleric acidemia.

The identification of (E)-2-methylglutaconic acid, a new isoleucine metabolite, in the urine of patients with beta-ketothiolase deficiency, propionic acidaemia and methylmalonic acidaemia.

Excretion of N-isovalerylglutamic acid in isovaleric acidemia.

Branched-chain amino acid supplementation and the immune response of long-distance athletes.

Identification of 19 new metabolites induced by abnormal amino acid conjugation in isovaleric acidemia.

The depletion of tryptophan and serotonin in the brain of developing hyperphenylalaninemic rats is abolished by the additional administration of lysine.

P2888

sj.ejcn.1602648

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1323-1327

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scholarly article

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10.1038/SJ.EJCN.1602648

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6506874

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17299485

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Amino-acid depletion induced by abnormal amino-acid conjugation and protein restriction in isovaleric acidemia.

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P2860

P2860

Amino-acid depletion induced by abnormal amino-acid conjugation and protein restriction in isovaleric acidemia.

description

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type

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prefLabel

P1433

P1476

P2093

P2860

P2888

P304

P31

P356

P433

P478

P577

P5875

P698

P356

P1433

P1476

P2093

P2860

P2888

P304

P31

P356

P433

P478

P577

P5875

P698