Interaction between Multimeric von Willebrand Factor and Complement: A Fresh Look to the Pathophysiology of Microvascular Thrombosis.

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Acquired thrombotic thrombocytopenic purpura with isolated CFHR3/1 deletion-rapid remission following complement blockade.

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Interaction between Multimeric von Willebrand Factor and Complement: A Fresh Look to the Pathophysiology of Microvascular Thrombosis.

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2017 nî lūn-bûn

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2017年の論文

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年學術文章

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2017年學術文章

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name

Interaction between Multimeric ...... y of Microvascular Thrombosis.

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Interaction between Multimeric ...... y of Microvascular Thrombosis.

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Interaction between Multimeric ...... y of Microvascular Thrombosis.

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Interaction between Multimeric ...... y of Microvascular Thrombosis.

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Interaction between Multimeric ...... y of Microvascular Thrombosis.

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Interaction between Multimeric ...... y of Microvascular Thrombosis.

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P1476

Interaction between Multimeric ...... y of Microvascular Thrombosis.

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P2093

Agustin Tortajada

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Caterina Mele

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Chiara Tentori

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Elena Bresin

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Marta Alberti

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Miriam Galbusera

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Roberta Donadelli

http://www.w3.org/2001/XMLSchema#string

Sara Gastoldi

http://www.w3.org/2001/XMLSchema#string

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Relative role of genetic complement abnormalities in sporadic and familial aHUS and their impact on clinical phenotype

Association of factor H autoantibodies with deletions of CFHR1, CFHR3, CFHR4, and with mutations in CFH, CFI, CD46, and C3 in patients with atypical hemolytic uremic syndrome

Factor B structure provides insights into activation of the central protease of the complement system

Alternative pathway activation of complement by Shiga toxin promotes exuberant C3a formation that triggers microvascular thrombosis

Calcium-dependent conformational flexibility of a CUB domain controls activation of the complement serine protease C1r

Structural basis for the stabilization of the complement alternative pathway C3 convertase by properdin.

Increased plasma thrombomodulin as a vascular endothelial cell marker in patients with thrombotic thrombocytopenic purpura and hemolytic uremic syndrome.

Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura.

von Willebrand factor cleaving protease (ADAMTS13) is deficient in recurrent and familial thrombotic thrombocytopenic purpura and hemolytic uremic syndrome.

Epitope mapping of ADAMTS13 autoantibodies in acquired thrombotic thrombocytopenic purpura.

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1021-1040

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scholarly article

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10.4049/JIMMUNOL.1601121

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English

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199

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2017-06-26T00:00:00Z

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28652401

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P921

pathophysiology

thrombosis

Interaction between Multimeric von Willebrand Factor and Complement: A Fresh Look to the Pathophysiology of Microvascular Thrombosis.

about

P2860

P2860

Interaction between Multimeric von Willebrand Factor and Complement: A Fresh Look to the Pathophysiology of Microvascular Thrombosis.

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