Neurodevelopmental consequences of Smn depletion in a mouse model of spinal muscular atrophy.
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The contribution of mouse models to understanding the pathogenesis of spinal muscular atrophyTemporal requirement for SMN in motoneuron development.Somatic Therapy of a Mouse SMA Model with a U7 snRNA Gene Correcting SMN2 SplicingThe Smn-independent beneficial effects of trichostatin A on an intermediate mouse model of spinal muscular atrophy.Transcriptome profiling of spinal muscular atrophy motor neurons derived from mouse embryonic stem cellsModeling spinal muscular atrophy in Drosophila links Smn to FGF signalingSelective vulnerability of spinal and cortical motor neuron subpopulations in delta7 SMA mice.Splicing changes in SMA mouse motoneurons and SMN-depleted neuroblastoma cells: evidence for involvement of splicing regulatory proteins.Mouse models of SMA: tools for disease characterization and therapeutic development.Spinal muscular atrophy: a motor neuron disorder or a multi-organ disease?Invited review: decoding the pathophysiological mechanisms that underlie RNA dysregulation in neurodegenerative disorders: a review of the current state of the art.A novel role for CARM1 in promoting nonsense-mediated mRNA decay: potential implications for spinal muscular atrophy.Diverse role of survival motor neuron protein.Supraphysiological expression of survival motor neuron protein from an adenovirus vector does not adversely affect cell function.Hypoxia is a modifier of SMN2 splicing and disease severity in a severe SMA mouse modelAlpha-synuclein loss in spinal muscular atrophySmn deficiency causes neuritogenesis and neurogenesis defects in the retinal neurons of a mouse model of spinal muscular atrophy.Axon outgrowth and neuronal differentiation defects after a-SMN and FL-SMN silencing in primary hippocampal cultures.Cell-type-specific miR-431 dysregulation in a motor neuron model of spinal muscular atrophy
P2860
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P2860
Neurodevelopmental consequences of Smn depletion in a mouse model of spinal muscular atrophy.
description
2010 nî lūn-bûn
@nan
2010年の論文
@ja
2010年学术文章
@wuu
2010年学术文章
@zh
2010年学术文章
@zh-cn
2010年学术文章
@zh-hans
2010年学术文章
@zh-my
2010年学术文章
@zh-sg
2010年學術文章
@yue
2010年學術文章
@zh-hant
name
Neurodevelopmental consequence ...... el of spinal muscular atrophy.
@en
Neurodevelopmental consequence ...... el of spinal muscular atrophy.
@nl
type
label
Neurodevelopmental consequence ...... el of spinal muscular atrophy.
@en
Neurodevelopmental consequence ...... el of spinal muscular atrophy.
@nl
prefLabel
Neurodevelopmental consequence ...... el of spinal muscular atrophy.
@en
Neurodevelopmental consequence ...... el of spinal muscular atrophy.
@nl
P2093
P356
P1476
Neurodevelopmental consequence ...... el of spinal muscular atrophy.
@en
P2093
Dina Shafey
Justin N Moores
P2860
P304
P356
10.1002/JNR.22189
P577
2010-01-01T00:00:00Z