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EPM2A:PPP1R3C:glycogen-GYG1:GYS1-a tetramer
EPM2A:PPP1R3C:glycogen-GYG1:GYS1-a tetramer
Item
http://www.wikidata.org/entity/Q50256339
Q50256339
about
Defective NHLRC1 does not ubiquitinate EPM2A (laforin) and PPP1R3C (PTG) (type 2B disease)
EPM2A dimer dephosphorylates phosphoglycogen-GYG1
NHLRC1 mediated ubiquitination of EPM2A and PPP1RC3 associated with glycogen-GYG1
P527
Q50289091-6B7F5C21-27BA-4EED-B08D-73C9B5E1E11C
Q50293102-B61348B5-1566-4CA5-B81A-9204014D424F
Q50293105-D2CBA822-A2AD-4B41-95EA-70FD83E636A3
P527
EPM2A:PPP1R3C:glycogen-GYG1:GYS1-a tetramer
Item
http://www.wikidata.org/entity/Q50256339
description
Macromolecular complex
@en
name
EPM2A:PPP1R3C:glycogen-GYG1:GYS1-a tetramer
@en
type
Item
label
EPM2A:PPP1R3C:glycogen-GYG1:GYS1-a tetramer
@en
prefLabel
EPM2A:PPP1R3C:glycogen-GYG1:GYS1-a tetramer
@en
P2888
Q50256339-EA929E26-BBA6-4BE6-A244-E7E6911F0AAA
P31
Q50256339-34534878-E8AF-42A9-88F6-461E44EEABBE
P3937
Q50256339-4A991A0A-E481-43C6-B2DF-94EE983AE731
P527
Q50256339-8B5963F6-F1D2-4EDF-9DFB-84EB47CCD2F5
Q50256339-9F720543-55AB-41E5-85C4-B8296FCC919C
Q50256339-DFAD7BA1-A694-40B4-9BC3-AFB4F5D8FFB3
Q50256339-E1B5669D-A648-48DB-80D4-0DEEB93B7DDF
P703
Q50256339-D93C1F7E-C79A-4E4D-AB77-0FE41570462F
P2888
reactome:R-HSA-3781000
P31
protein complex
P3937
R-HSA-3781000
http://www.w3.org/2001/XMLSchema#string
P527
Glycogen synthase 1
Protein phosphatase 1 regulatory subunit 3C
magnesium cation
EPM2A dimer
P703
Homo sapiens