Targeted pharmacotherapy in progressive familial intrahepatic cholestasis type 2: Evidence for improvement of cholestasis with 4-phenylbutyrate.
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Liver transplantation and the management of progressive familial intrahepatic cholestasis in childrenRecent advances in understanding and managing cholestasisFunctional Rescue of Trafficking-Impaired ABCB4 Mutants by Chemical Chaperones4-PBA prevents pressure overload-induced myocardial hypertrophy and interstitial fibrosis by attenuating endoplasmic reticulum stressGeneration of a bile salt export pump deficiency model using patient-specific induced pluripotent stem cell-derived hepatocyte-like cellsRecent advances in the exploration of the bile salt export pump (BSEP/ABCB11) function.Current and future therapies for inherited cholestatic liver diseases.New therapeutic concepts in bile acid transport and signaling for management of cholestasis.Exon-skipping and mRNA decay in human liver tissue: molecular consequences of pathogenic bile salt export pump mutations.Bipolar and Related Disorders Induced by Sodium 4-Phenylbutyrate in a Male Adolescent with Bile Salt Export Pump Deficiency Disease.Genetic profiling of children with advanced cholestatic liver disease.Functional Rescue of ABCC6 Deficiency by 4-Phenylbutyrate Therapy Reduces Dystrophic Calcification in Abcc6-/- Mice.Clinically relevant mutations in the ABCG2 transporter uncovered by genetic analysis linked to erythrocyte membrane protein expression.New Insights in Genetic Cholestasis: From Molecular Mechanisms to Clinical Implications
P2860
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P2860
Targeted pharmacotherapy in progressive familial intrahepatic cholestasis type 2: Evidence for improvement of cholestasis with 4-phenylbutyrate.
description
2015 nî lūn-bûn
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2015年の論文
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2015年学术文章
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name
Targeted pharmacotherapy in pr ...... estasis with 4-phenylbutyrate.
@en
Targeted pharmacotherapy in pr ...... estasis with 4-phenylbutyrate.
@nl
type
label
Targeted pharmacotherapy in pr ...... estasis with 4-phenylbutyrate.
@en
Targeted pharmacotherapy in pr ...... estasis with 4-phenylbutyrate.
@nl
prefLabel
Targeted pharmacotherapy in pr ...... estasis with 4-phenylbutyrate.
@en
Targeted pharmacotherapy in pr ...... estasis with 4-phenylbutyrate.
@nl
P2093
P2860
P356
P1433
P1476
Targeted pharmacotherapy in pr ...... estasis with 4-phenylbutyrate.
@en
P2093
Anne Davit-Spraul
Brice Schuller
Brigitte Grosse
Doris Cassio
Emmanuel Gonzales
Filomena Conti
P2860
P304
P356
10.1002/HEP.27767
P407
P577
2015-02-26T00:00:00Z