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Q28475804-65759FF5-782C-4533-B7FA-D4CE0B8EE445
Q28475804-65759FF5-782C-4533-B7FA-D4CE0B8EE445
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http://www.wikidata.org/entity/statement/Q28475804-65759FF5-782C-4533-B7FA-D4CE0B8EE445
The first cellular models based on frataxin missense mutations that reproduce spontaneously the defects associated with Friedreich ataxia
P2860
Q28475804-65759FF5-782C-4533-B7FA-D4CE0B8EE445
BestRank
Statement
http://www.wikidata.org/entity/statement/Q28475804-65759FF5-782C-4533-B7FA-D4CE0B8EE445
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wasDerivedFrom
79fa333d51f2c318762e13ddfb4c87369b13d311
P2860
The Friedreich's ataxia mutation confers cellular sensitivity to oxidant stress which is rescued by chelators of iron and calcium and inhibitors of apoptosis.