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Q34178677-0DE439E5-8358-451B-94A2-EB126D6E5459
Q34178677-0DE439E5-8358-451B-94A2-EB126D6E5459
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http://www.wikidata.org/entity/statement/Q34178677-0DE439E5-8358-451B-94A2-EB126D6E5459
The collagen VI-related myopathies Ullrich congenital muscular dystrophy and Bethlem myopathy.
P2860
Q34178677-0DE439E5-8358-451B-94A2-EB126D6E5459
BestRank
Statement
http://www.wikidata.org/entity/statement/Q34178677-0DE439E5-8358-451B-94A2-EB126D6E5459
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wasDerivedFrom
a78325e9ac796ffbafa90921d65d54618c8a636d
P2860
The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice.