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Q35776562-B0230136-B7ED-472D-9485-AD88BB0EF415
Q35776562-B0230136-B7ED-472D-9485-AD88BB0EF415
BestRank
Statement
http://www.wikidata.org/entity/statement/Q35776562-B0230136-B7ED-472D-9485-AD88BB0EF415
Dipeptide repeat protein inclusions are rare in the spinal cord and almost absent from motor neurons in C9ORF72 mutant amyotrophic lateral sclerosis and are unlikely to cause their degeneration.
P2860
Q35776562-B0230136-B7ED-472D-9485-AD88BB0EF415
BestRank
Statement
http://www.wikidata.org/entity/statement/Q35776562-B0230136-B7ED-472D-9485-AD88BB0EF415
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type
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wasDerivedFrom
791a4bcb9361b5aa4c2eec2240f1e2b9d0bb9194
P2860
Antisense proline-arginine RAN dipeptides linked to C9ORF72-ALS/FTD form toxic nuclear aggregates that initiate in vitro and in vivo neuronal death.