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Q47073900-0675701E-CDAB-4FBE-B8ED-EAD704C84F5A
Q47073900-0675701E-CDAB-4FBE-B8ED-EAD704C84F5A
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Statement
http://www.wikidata.org/entity/statement/Q47073900-0675701E-CDAB-4FBE-B8ED-EAD704C84F5A
A zebrafish model of CLN2 disease is deficient in tripeptidyl peptidase 1 and displays progressive neurodegeneration accompanied by a reduction in proliferation.
P2860
Q47073900-0675701E-CDAB-4FBE-B8ED-EAD704C84F5A
BestRank
Statement
http://www.wikidata.org/entity/statement/Q47073900-0675701E-CDAB-4FBE-B8ED-EAD704C84F5A
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wasDerivedFrom
d1427a0d8c846c5d996099cbfeb78118e329eca7
P2860
A lysosomal proteinase, the late infantile neuronal ceroid lipofuscinosis gene (CLN2) product, is essential for degradation of a hydrophobic protein, the subunit c of ATP synthase.