about
Mitochondrial Fatty Acid Beta-Oxidationmitochondrial fatty acid beta-oxidation of saturated fatty acidsBeta oxidation of palmitoyl-CoA to myristoyl-CoABeta oxidation of myristoyl-CoA to lauroyl-CoABeta oxidation of lauroyl-CoA to decanoyl-CoA-CoABeta oxidation of decanoyl-CoA to octanoyl-CoA-CoABeta oxidation of octanoyl-CoA to hexanoyl-CoABeta oxidation of hexanoyl-CoA to butanoyl-CoABeta oxidation of butanoyl-CoA to acetyl-CoAmitochondrial fatty acid beta-oxidation of unsaturated fatty acidsLinoleoyl-CoA is converted to cis;cis-3;6- dodecadienoyl-CoA by three cycles of beta-oxidationTrans;cis-lauro-2;6-dienoyl-CoA is converted to cis;cis-3;6- 4-cis-decenoyl-CoA by one cycle of beta-oxidationdehydrogenation of 4-cis-decenoyl-CoA to form 2-trans-4-cis-decadienoyl-CoAReduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoAIsomerization of 3-trans-decenoyl-CoA to form trans-dec-2-enoyl-CoA
P31
Ethylmalonyl-CoA decarboxylase 1Adiponectin, C1Q and collagen domain containingCarnitine palmitoyltransferase 2ATP-binding cassette, sub-family D (ALD), member 1Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit betaAcetyl-Coenzyme A acetyltransferase 1Acyl-CoA oxidase 3, pristanoylAcyl-CoA oxidase 1Acyl-CoA oxidase 2Acyl-CoA oxidase likeEnoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase2,4-dienoyl-CoA reductase 1Carnitine palmitoyltransferase 1ACarnitine palmitoyltransferase 1CMitochondrial trans-2-enoyl-CoA reductaseCarnitine O-octanoyltransferaseAcyl-CoA dehydrogenase family member 10Acyl-CoA dehydrogenase family member 11Carnitine palmitoyltransferase 1B3-hydroxyisobutyryl-CoA hydrolaseMalonyl-CoA-acyl carrier protein transacylaseAU RNA binding methylglutaconyl-CoA hydrataseEnoyl-CoA delta isomerase 2Enoyl-CoA hydratase, short chain 1Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alphaEnoyl-CoA delta isomerase 1Enoyl-CoA hydratase 1ATP binding cassette subfamily D member 3ATP binding cassette subfamily D member 2Acyl-CoA dehydrogenase medium chainAcyl-CoA dehydrogenase short chainAcyl-CoA dehydrogenase long chain3-hydroxybutyrate dehydrogenase 2Hydroxyacyl-CoA dehydrogenaseAcyl-CoA dehydrogenase very long chainHydroxysteroid 17-beta dehydrogenase 4Acetyl-CoA acyltransferase 1Acetyl-CoA acetyltransferase 2Solute carrier family 27 member 2Peroxisomal biogenesis factor 7
P682
PPAR delta: an uncompletely known nuclear receptorAdrenoleukodystrophy: subcellular localization and degradation of adrenoleukodystrophy protein (ALDP/ABCD1) with naturally occurring missense mutationsHuman mitochondrial 3,2-trans-enoyl-CoA isomerase (DCI): gene structure and localization to chromosome 16p13.3cDNA cloning of the human peroxisomal enoyl-CoA hydratase: 3-hydroxyacyl-CoA dehydrogenase bifunctional enzyme and localization to chromosome 3q26.3-3q28: a free left Alu Arm is inserted in the 3' noncoding regionIdentification of a common mutation in patients with medium-chain acyl-CoA dehydrogenase deficiencyRhizomelic chondrodysplasia punctata. Deficiency of 3-oxoacyl-coenzyme A thiolase in peroxisomes and impaired processing of the enzymeClinical, biochemical and metabolic characterisation of a mild form of human short-chain enoyl-CoA hydratase deficiency: significance of increased N-acetyl-S-(2-carboxypropyl)cysteine excretionPeroxisomal fatty acid oxidation disorders and 58 kDa sterol carrier protein X (SCPx). Activity measurements in liver and fibroblasts using a newly developed methodImportant Trends in UCP3 InvestigationRole of common gene variations in the molecular pathogenesis of short-chain acyl-CoA dehydrogenase deficiency
P921
Q45317247-6A087F79-22E0-448E-82CD-A48209FD672BQ45317249-9E017631-2762-4B0C-8DBE-8A8D0C134CE2Q45317250-B4E4917C-DE43-43C7-B288-C4536F419F40Q45317252-55828B8C-2CE8-432E-B8ED-92CD50C84FF5Q45317254-9C627574-96CB-46E3-823E-1817BD5AAFE5Q45317255-42C1D9E6-2E7F-4E7A-B568-22A96ACE532BQ45317256-2A1043BF-5173-4BDC-82FD-DA095EABB2BCQ45317257-145C2F61-438E-4A0E-9F91-B6FA46FC03C5Q45317258-7D85F6A4-C57B-403C-A37E-1DF909ED7697Q45317260-C06BB1E6-F8FA-4582-91F5-C0DB4F5BFD95Q50293653-30913B49-5832-498D-AA23-180A85D36F83Q50293655-9B0D34D0-D844-4DA7-B91B-2FA8100E136FQ50293657-A116DAAF-9D3C-4108-AA1B-693A9A7D70FFQ50293658-D56EF443-8720-4E68-9AC0-FFCD82629913Q50293659-6A95F8F3-E0C1-47F7-9AF6-33541B3D2BA3
P31
Q13365951-1C2C4DFB-02E8-48C7-B1BF-8DFD0EA7F39EQ14864062-997ED24D-5B92-4ADF-9218-E68F591322BDQ14912539-45F87F6F-0A30-4FB9-89D6-A638CE967422Q14912816-149ADE42-0F30-47A3-92F1-5BA45879DAD2Q14912816-E7A5D2F1-5841-4F2E-9534-FF3B541B85EFQ14912988-19E49FD8-F059-4A3A-BBCD-CB806F245611Q14912988-4C9EAB6E-0A29-4819-B77A-6982057566EAQ14913203-6442D51D-8A53-4685-957E-8974DA55C3DFQ21096281-80ADBA1A-0233-4B58-80F6-65FC4C9AE2E1Q21096304-A2828D1C-86DA-45CF-9F53-C3CB22B4F363Q21096342-9DBE891E-904F-44F2-8FB2-2E07F1680E0BQ21096344-3D0D6DD9-1CB8-48A4-ADC0-1E86359E2014Q21096438-69F37B35-74A5-4872-83E8-5B6BFE05FE64Q21101067-FC2A387F-78A5-41C7-90E7-E9E0F24C85B3Q21106909-BC00FBDD-0F10-4BBF-88C6-4D7B3DF75AE1Q21106939-853C59F4-151E-44A4-9B74-1412561AC9E0Q21108933-885335D3-C525-4C76-9A88-26FE929924F6Q21109101-16B39BA2-A063-458F-9985-CA488B4BD19DQ21109382-4BE7FB94-85AD-4A7A-A581-F3D083C27E8DQ21109386-6CEBB7A9-860E-4CDC-9173-E6453D3251D3Q21110591-6B572D36-5F56-4A99-BCFB-86F96DBB77B8Q21111026-7D453C14-2B78-414B-99A0-CD5774EE215BQ21112413-2384FA8F-A76D-4329-8B7B-7F749C60FC4CQ21112722-E257D138-7FF5-4DA9-BD37-54906964DAA3Q21113217-325233EF-6DA8-492A-9933-0B4C166ABE29Q21113219-6E0AC5A5-FBD3-4ADE-90B5-477FBC1DD6AFQ21113219-826E4B09-3FAE-407D-B711-CAAAE80988EEQ21113220-19031D82-886F-41DF-A087-706499C67613Q21113220-4744172A-D343-485D-91D5-D55C6FC273B2Q21113220-9085C649-04FE-4D5A-9267-89EE23381B33Q21113222-B3D22AE6-AFB9-4A8F-B11F-B0ECC39DE180Q21113226-74AE6794-6AFC-44BB-8A59-7744C4727BF6Q21113663-58D98D85-514A-4D2D-9824-5DE30CB613ABQ21113681-4003CBFF-150A-4B8D-B48C-A5D58BD40074Q21113690-A35BC142-242A-4CF5-9094-8676DB1537D7Q21113690-E3BCFAB7-EC45-45D3-8BB8-976208D6BB7BQ21113693-4E6CFC22-AE8E-4BD7-B7FE-EB2B6E0FFF97Q21113696-36C7B05D-A63F-49F7-9365-E3C6B8A1E6A6Q21113904-E9D8B115-2198-4535-A0D3-99EF8DCBD818Q21114675-58233048-DC5C-4956-90D2-3C69536F6ABC
P682
description
A fatty acid oxidation process ...... tions during each of which the
@en
biologisch proces
@nl
name
fatty acid beta-oxidation
@en
type
label
fatty acid beta-oxidation
@en
altLabel
GO:0006635
@en
prefLabel
fatty acid beta-oxidation
@en
P2888
P686
GO:0006635