Alterations in lipid metabolism gene expression and abnormal lipid accumulation in fibroblast explants from giant axonal neuropathy patients
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Lipid droplets, perilipins and cytokeratins--unravelled liaisons in epithelium-derived cellsGiant axonal neuropathy: An updated perspective on its pathology and pathogenesis.Sensory-motor deficits and neurofilament disorganization in gigaxonin-null mice.Giant axonal neuropathy-associated gigaxonin mutations impair intermediate filament protein degradation.Modest loss of peripheral axons, muscle atrophy and formation of brain inclusions in mice with targeted deletion of gigaxonin exon 1Gigaxonin controls vimentin organization through a tubulin chaperone-independent pathway.Onset of human cytomegalovirus replication in fibroblasts requires the presence of an intact vimentin cytoskeleton.Explaining intermediate filament accumulation in giant axonal neuropathyProteomic analysis in giant axonal neuropathy: new insights into disease mechanisms.
P2860
Q27321346-BF218A65-5500-46D1-8587-CFC36C8234AFQ30363784-62D2BA13-F9B0-4630-94DD-608A26367D95Q34980848-0236B2E0-82DC-4C4B-8A1C-82661F2A9D27Q36793478-D8493E54-6053-4EA0-9B1D-005B57F62E87Q36853945-F737E487-E946-4F29-B57E-17F9E99BBDA6Q37147147-D6F48B3B-6A91-447B-AC4C-7DFB65B33A58Q41881987-A0C62281-D98B-417C-94C2-51E8A2346725Q41962129-7BF6A727-2816-4306-8BDC-144DB382E08FQ49159532-93392780-C46B-4A8B-9CA3-72798FE8B7CC
P2860
Alterations in lipid metabolism gene expression and abnormal lipid accumulation in fibroblast explants from giant axonal neuropathy patients
description
2007 nî lūn-bûn
@nan
2007 թուականին հրատարակուած գիտական յօդուած
@hyw
2007 թվականին հրատարակված գիտական հոդված
@hy
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
name
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@ast
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@en
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@en-gb
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@nl
type
label
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@ast
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@en
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@en-gb
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@nl
prefLabel
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@ast
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@en
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@en-gb
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@nl
P2093
P2860
P356
P1433
P1476
Alterations in lipid metabolis ...... ant axonal neuropathy patients
@en
P2093
Conrad L Leung
Dmitry Goryunov
Ronald K H Liem
Yinghua Pang
P2860
P2888
P356
10.1186/1471-2156-8-6
P407
P577
2007-01-01T00:00:00Z
P5875
P6179
1041069174