MCD encodes peroxisomal and cytoplasmic forms of malonyl-CoA decarboxylase and is mutated in malonyl-CoA decarboxylase deficiency
about
The identification of a succinyl-CoA thioesterase suggests a novel pathway for succinate production in peroxisomesStructural Asymmetry and Disulfide Bridges among Subunits Modulate the Activity of Human Malonyl-CoA DecarboxylaseCrystal Structures of Malonyl-Coenzyme A Decarboxylase Provide Insights into Its Catalytic Mechanism and Disease-Causing MutationsFatal malonyl CoA decarboxylase deficiency due to maternal uniparental isodisomy of the telomeric end of chromosome 16Malonyl-CoA decarboxylase is present in the cytosolic, mitochondrial and peroxisomal compartments of rat hepatocytesMetabolic cardiomyopathies.Exercise training decreases the concentration of malonyl-CoA and increases the expression and activity of malonyl-CoA decarboxylase in human muscle.Chemical-genetic induction of Malonyl-CoA decarboxylase in skeletal muscle.Metabolic Encephalopathy and Lipid Storage Myopathy Associated with a Presumptive Mitochondrial Fatty Acid Oxidation Defect in a Dog.The malonyl CoA axis as a potential target for treating ischaemic heart disease.Peroxisome biogenesis: something old, something new, something borrowed.Peroxisomal-proliferator-activated receptor alpha activates transcription of the rat hepatic malonyl-CoA decarboxylase gene: a key regulation of malonyl-CoA level.Protein acetylation in metabolism - metabolites and cofactors.Malonyl-CoA decarboxylase inhibition is selectively cytotoxic to human breast cancer cells.New insights into the distribution, protein abundance and subcellular localisation of the endogenous peroxisomal biogenesis proteins PEX3 and PEX19 in different organs and cell types of the adult mouse.Characterization of rat liver malonyl-CoA decarboxylase and the study of its role in regulating fatty acid metabolismMalonic aciduria: long-term follow-up of new patients detected by newborn screening.Malonyl CoA decarboxylase deficiency: C to T transition in intron 2 of the MCD gene.In-depth proteome analysis of Arabidopsis leaf peroxisomes combined with in vivo subcellular targeting verification indicates novel metabolic and regulatory functions of peroxisomes.A role for hypothalamic malonyl-CoA in the control of food intake.malonyl-CoA is decarboxylated to acetyl-CoA in peroxisomeIdentification of the active site of human mitochondrial malonyl-coenzyme a decarboxylase: A combined computational study.A new case of malonyl-CoA decarboxylase deficiency with mild clinical features.
P2860
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P2860
MCD encodes peroxisomal and cytoplasmic forms of malonyl-CoA decarboxylase and is mutated in malonyl-CoA decarboxylase deficiency
description
1999 nî lūn-bûn
@nan
1999 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
1999 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
1999年の論文
@ja
1999年論文
@yue
1999年論文
@zh-hant
1999年論文
@zh-hk
1999年論文
@zh-mo
1999年論文
@zh-tw
1999年论文
@wuu
name
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@ast
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@en
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@en-gb
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@nl
type
label
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@ast
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@en
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@en-gb
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@nl
prefLabel
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@ast
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@en
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@en-gb
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@nl
P2093
P356
P1476
MCD encodes peroxisomal and cy ...... l-CoA decarboxylase deficiency
@en
P2093
J C Morrell
K A Sacksteder
R J Wanders
P304
P356
10.1074/JBC.274.35.24461
P407
P577
1999-08-27T00:00:00Z