Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
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Standard (head-down tilt) versus modified (without head-down tilt) postural drainage in infants and young children with cystic fibrosisSodium channel blockers for cystic fibrosisAntibiotic treatment for Burkholderia cepacia complex in people with cystic fibrosis experiencing a pulmonary exacerbationTopical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung diseaseSodium channel blockers for cystic fibrosisStandard versus modified postural drainage in infants and young children with cystic fibrosisTopical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung diseaseMacrolide antibiotics for cystic fibrosisMacrolide antibiotics for cystic fibrosisAntibiotic treatment for Burkholderia cepacia complex in people with cystic fibrosis experiencing a pulmonary exacerbationTopical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung diseaseTopical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung diseaseSodium channel blockers for cystic fibrosisMacrolide antibiotics for cystic fibrosisMacrolide antibiotics for cystic fibrosisIdentification of dynein heavy chain 7 as an inner arm component of human cilia that is synthesized but not assembled in a case of primary ciliary dyskinesiaDifferential effects of Hsc70 and Hsp70 on the intracellular trafficking and functional expression of epithelial sodium channelsEffects of reduced mucus oxygen concentration in airway Pseudomonas infections of cystic fibrosis patientsTissue damage detection by osmotic surveillanceAirway surface liquid volume regulation determines different airway phenotypes in liddle compared with betaENaC-overexpressing miceTransgenic hCFTR expression fails to correct β-ENaC mouse lung diseaseRescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770A polymicrobial perspective of pulmonary infections exposes an enigmatic pathogen in cystic fibrosis patientsCystic fibrosisThe lactoperoxidase system links anion transport to host defense in cystic fibrosisAirway epithelial cell tolerance to Pseudomonas aeruginosa.'CFTR-opathies': disease phenotypes associated with cystic fibrosis transmembrane regulator gene mutationsSafety assessment of inhaled xylitol in mice and healthy volunteersState of the art: why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection?Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung diseaseEpithelial Anion Transport as Modulator of Chemokine SignalingCurrent and future treatment options for cystic fibrosis lung disease: latest evidence and clinical implicationsAirway epithelial repair in health and disease: Orchestrator or simply a player?Mucociliary dysfunction in HIV and smoked substance abuseTargeted therapies to improve CFTR function in cystic fibrosisInhaled hypertonic saline for cystic fibrosis: Reviewing the potential evidence for modulation of neutrophil signalling and functionMicroscale imaging of cilia-driven fluid flowCystic fibrosis transmembrane conductance regulator dysfunction and its treatmentPathogenesis of acute respiratory illness caused by human parainfluenza virusesLoss of cftr function leads to pancreatic destruction in larval zebrafish.
P2860
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P2860
Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
description
1998 nî lūn-bûn
@nan
1998 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
1998 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
1998年の論文
@ja
1998年学术文章
@wuu
1998年学术文章
@zh-cn
1998年学术文章
@zh-hans
1998年学术文章
@zh-my
1998年学术文章
@zh-sg
1998年學術文章
@yue
name
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@ast
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@en
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@en-gb
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@nl
type
label
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@ast
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@en
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@en-gb
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@nl
prefLabel
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@ast
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@en
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@en-gb
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@nl
P2093
P3181
P1433
P1476
Evidence for periciliary liqui ...... ystic fibrosis airways disease
@en
P2093
R C Boucher
S H Randell
P304
P3181
P356
10.1016/S0092-8674(00)81724-9
P407
P577
1998-12-23T00:00:00Z