Human adrenoleukodystrophy protein and related peroxisomal ABC transporters interact with the peroxisomal assembly protein PEX19p
about
Defective peroxisome membrane synthesis due to mutations in human PEX3 causes Zellweger syndrome, complementation group GIn vitro transport of membrane proteins to peroxisomes by shuttling receptor Pex19pMutations in ABCD4 cause a new inborn error of vitamin B12 metabolismCharacterization of the interaction between recombinant human peroxin Pex3p and Pex19p: identification of TRP-104 IN Pex3p as a critical residue for the interactionAdrenoleukodystrophy: subcellular localization and degradation of adrenoleukodystrophy protein (ALDP/ABCD1) with naturally occurring missense mutationsPEX3 functions as a PEX19 docking factor in the import of class I peroxisomal membrane proteinsLive cell FRET microscopy: homo- and heterodimerization of two human peroxisomal ABC transporters, the adrenoleukodystrophy protein (ALDP, ABCD1) and PMP70 (ABCD3)Interaction of a farnesylated protein with renal type IIa Na/Pi co-transporter in response to parathyroid hormone and dietary phosphateHuman pex19p binds peroxisomal integral membrane proteins at regions distinct from their sorting sequencesLarge-scale mapping of human protein-protein interactions by mass spectrometryPotential role for Pex19p in assembly of PTS-receptor docking complexesDomain architecture and activity of human Pex19p, a chaperone-like protein for intracellular trafficking of peroxisomal membrane proteinsAdrenoleukodystrophy and related disorders.Genetic and molecular bases of peroxisome biogenesis disorders.Integrative analyses of genetic variation, epigenetic regulation, and the transcriptome to elucidate the biology of platinum sensitivityMammalian peroxisomal ABC transporters: from endogenous substrates to pathology and clinical significance.Function of the PEX19-binding site of human adrenoleukodystrophy protein as targeting motif in man and yeast. PMP targeting is evolutionarily conserved.Predictive Structure and Topology of Peroxisomal ATP-Binding Cassette (ABC) Transporters.Peroxisomal ATP-binding cassette transporters form mainly tetramers.Trypanosoma brucei glycosomal ABC transporters: identification and membrane targeting.Identification of a new fatty acid synthesis-transport machinery at the peroxisomal membrane.S149R, a novel mutation in the ABCD1 gene causing X-linked adrenoleukodystrophy.Functional characterization of the adrenoleukodystrophy protein (ALDP) and disease pathogenesis.PEX-19 docks ABCD1/D2/D3 to peroximal membraneABCD1-3 dimers transfer LCFAs from cytosol to peroxisomal matrixHydrophobic regions adjacent to transmembrane domains 1 and 5 are important for the targeting of the 70-kDa peroxisomal membrane protein.Linking mutated primary structure of adrenoleukodystrophy protein with X-linked adrenoleukodystrophy.
P2860
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P2860
Human adrenoleukodystrophy protein and related peroxisomal ABC transporters interact with the peroxisomal assembly protein PEX19p
description
2000 nî lūn-bûn
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2000 թուականի Ապրիլին հրատարակուած գիտական յօդուած
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2000 թվականի ապրիլին հրատարակված գիտական հոդված
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2000年の論文
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2000年論文
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2000年論文
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name
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@ast
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@en
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@en-gb
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@nl
type
label
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@ast
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@en
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@en-gb
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@nl
prefLabel
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@ast
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@en
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@en-gb
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@nl
P2093
P356
P1476
Human adrenoleukodystrophy pro ...... isomal assembly protein PEX19p
@en
P2093
A A Roscher
A C Muntau
A Holzinger
J K Gerber
P Landgraf
P U Mayerhofer
S Kammerer
P304
P356
10.1006/BBRC.2000.2572
P407
P577
2000-04-29T00:00:00Z