The cardiolipin transacylase, tafazzin, associates with two distinct respiratory components providing insight into Barth syndrome - Test2 - elhamkhani - TriplyDB

The cardiolipin transacylase, tafazzin, associates with two distinct respiratory components providing insight into Barth syndrome

The cardiolipin transacylase, tafazzin, associates with two distinct respiratory components providing insight into Barth syndrome

http://www.wikidata.org/entity/Q24651872

about

Acyl coenzyme A thioesterase Them5/Acot15 is involved in cardiolipin remodeling and fatty liver development Making heads or tails of phospholipids in mitochondria Characterization of tafazzin splice variants from humans and fruit flies Cardiolipin membrane domains in prokaryotes and eukaryotes Successful management of Barth syndrome: a systematic review highlighting the importance of a flexible and multidisciplinary approach Deacylation on the matrix side of the mitochondrial inner membrane regulates cardiolipin remodeling.The genetic interactome of prohibitins: coordinated control of cardiolipin and phosphatidylethanolamine by conserved regulators in mitochondria.LPS impairs oxygen utilization in epithelia by triggering degradation of the mitochondrial enzyme Alcat1 Cardiolipin fingerprinting of leukocytes by MALDI-TOF/MS as a screening tool for Barth syndrome Defining functional classes of Barth syndrome mutation in humans Biosynthesis, remodeling and turnover of mitochondrial cardiolipin Cardiolipin remodeling: a regulatory hub for modulating cardiolipin metabolism and function The complexity of cardiolipin in health and disease The topology and regulation of cardiolipin biosynthesis and remodeling in yeast Cardiolipin, a critical determinant of mitochondrial carrier protein assembly and function.Barth syndrome mutations that cause tafazzin complex lability.Mitochondrial cardiolipin involved in outer-membrane protein biogenesis: implications for Barth syndrome.Yeast as a system for modeling mitochondrial disease mechanisms and discovering therapies.Yeast Coq9 controls deamination of coenzyme Q intermediates that derive from para-aminobenzoic acid.Saccharomyces cerevisiae porin pore forms complexes with mitochondrial outer membrane proteins Om14p and Om45p Tafazzins from Drosophila and mammalian cells assemble in large protein complexes with a short half-life.New clinical and molecular insights on Barth syndrome Seven functional classes of Barth syndrome mutation The physical state of lipid substrates provides transacylation specificity for tafazzin The role of cardiolipin in the structural organization of mitochondrial membranes.The power of yeast to model diseases of the powerhouse of the cell.The Taz1p transacylase is imported and sorted into the outer mitochondrial membrane via a membrane anchor domain.Unremodeled and remodeled cardiolipin are functionally indistinguishable in yeast.Formation and regulation of mitochondrial membranes.The clinical maze of mitochondrial neurology New developments on the functions of coenzyme Q in mitochondria.ORP5/ORP8 localize to endoplasmic reticulum-mitochondria contacts and are involved in mitochondrial function.Interaction of MDM33 with mitochondrial inner membrane homeostasis pathways in yeast.The mitochondrial quality control protein Yme1 is necessary to prevent defective mitophagy in a yeast model of Barth syndrome.Mitochondria influence CDR1 efflux pump activity, Hog1-mediated oxidative stress pathway, iron homeostasis, and ergosterol levels in Candida albicans.Deletion of the cardiolipin-specific phospholipase Cld1 rescues growth and life span defects in the tafazzin mutant: implications for Barth syndrome.Overexpression of mitochondrial oxodicarboxylate carrier (ODC1) preserves oxidative phosphorylation in a yeast model of Barth syndrome.Tafazzin knockdown causes hypertrophy of neonatal ventricular myocytes.Barth syndrome cardiomyopathy.Conserved Lipid and Small-Molecule Modulation of COQ8 Reveals Regulation of the Ancient Kinase-like UbiB Family.

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P2860

The cardiolipin transacylase, tafazzin, associates with two distinct respiratory components providing insight into Barth syndrome

http://www.wikidata.org/entity/Q24651872

description

2008 nî lūn-bûn

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2008 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած

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2008 թվականի դեկտեմբերին հրատարակված գիտական հոդված

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2008年の論文

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2008年論文

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2008年論文

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2008年論文

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2008年論文

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2008年論文

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The cardiolipin transacylase, ...... ng insight into Barth syndrome

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The cardiolipin transacylase, ...... ng insight into Barth syndrome

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MBC.E08-09-0896

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Molecular Biology of the Cell

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The cardiolipin transacylase, ...... ng insight into Barth syndrome

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P2093

Carla M Koehler

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J Michael McCaffery

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Joseph A Loo

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Pinmanee Boontheung

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Steven M Claypool

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P2860

Defective remodeling of cardiolipin and phosphatidylglycerol in Barth syndrome

Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients

Comparison of lymphoblast mitochondria from normal subjects and patients with Barth syndrome using electron microscopic tomography

Only one splice variant of the human TAZ gene encodes a functional protein with a role in cardiolipin metabolism

Membrane fusion and the lamellar-to-inverted-hexagonal phase transition in cardiolipin vesicle systems induced by divalent cations

Toward the complete yeast mitochondrial proteome: multidimensional separation techniques for mitochondrial proteomics.

Site-directed mutagenesis by overlap extension using the polymerase chain reaction

Isolation of monoclonal antibodies specific for human c-myc proto-oncogene product

Yeast cells depleted in Atp14p fail to assemble Atp6p within the ATP synthase and exhibit altered mitochondrial cristae morphology.

Mitochondrial mislocalization and altered assembly of a cluster of Barth syndrome mutant tafazzins

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18799610

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