The enigmatic role of tafazzin in cardiolipin metabolism
about
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidationMitochondria targeting of non-peroxidizable triphenylphosphonium conjugated oleic acid protects mouse embryonic cells against apoptosis: role of cardiolipin remodelingCardiac and skeletal muscle defects in a mouse model of human Barth syndromeMaking heads or tails of phospholipids in mitochondriaBarth Syndrome: From Mitochondrial Dysfunctions Associated with Aberrant Production of Reactive Oxygen Species to Pluripotent Stem Cell StudiesSuccessful management of Barth syndrome: a systematic review highlighting the importance of a flexible and multidisciplinary approachPhospholipase A2 enzymes: physical structure, biological function, disease implication, chemical inhibition, and therapeutic interventionA mitochondrial phosphatase required for cardiolipin biosynthesis: the PGP phosphatase Gep4.Regulation of mitochondrial phospholipids by Ups1/PRELI-like proteins depends on proteolysis and Mdm35.LPS impairs oxygen utilization in epithelia by triggering degradation of the mitochondrial enzyme Alcat1Defining functional classes of Barth syndrome mutation in humansDisorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genesCardiolipin remodeling: a regulatory hub for modulating cardiolipin metabolism and functionThe complexity of cardiolipin in health and diseaseCell biology. Metabolic control of cell deathBacteria, yeast, worms, and flies: exploiting simple model organisms to investigate human mitochondrial diseasesDevelopmental Sex Differences in the Metabolism of Cardiolipin in Mouse Cerebral Cortex MitochondriaDynamic simulation of cardiolipin remodeling: greasing the wheels for an interpretative approach to lipidomics.Comprehensive analysis of phospholipids and glycolipids in the opportunistic pathogen Enterococcus faecalisTafazzin (TAZ) promotes the tumorigenicity of cervical cancer cells and inhibits apoptosisA mathematical model for the determination of steady-state cardiolipin remodeling mechanisms using lipidomic data.The 3-methylglutaconic acidurias: what's new?Modeling the mitochondrial cardiomyopathy of Barth syndrome with induced pluripotent stem cell and heart-on-chip technologies.Mutations in the phospholipid remodeling gene SERAC1 impair mitochondrial function and intracellular cholesterol trafficking and cause dystonia and deafness.CLPB mutations cause 3-methylglutaconic aciduria, progressive brain atrophy, intellectual disability, congenital neutropenia, cataracts, movement disorderBarth syndrome mutations that cause tafazzin complex lability.Manganese superoxide dismutase: guardian of the powerhouse.Improved functional recovery to I/R injury in hearts from lipocalin-2 deficiency mice: restoration of mitochondrial function and phospholipids remodelingTurnover of nonessential fatty acids in cardiolipin from the rat heart.Mouse Tafazzin Is Required for Male Germ Cell Meiosis and Spermatogenesis.Myocardial regulation of lipidomic flux by cardiolipin synthase: setting the beat for bioenergetic efficiency.Tafazzin knockdown in mice leads to a developmental cardiomyopathy with early diastolic dysfunction preceding myocardial noncompaction.New clinical and molecular insights on Barth syndromeIntra-individual plasticity of the TAZ gene leading to different heritable mutations in siblings with Barth syndromeDysfunctional cardiac mitochondrial bioenergetic, lipidomic, and signaling in a murine model of Barth syndromeLeft ventricular noncompaction (LVNC) and low mitochondrial membrane potential are specific for Barth syndrome.Unremodeled and remodeled cardiolipin are functionally indistinguishable in yeast.Formation and regulation of mitochondrial membranes.Cardiological manifestations of mitochondrial respiratory chain disorders.Disorders of phospholipids, sphingolipids and fatty acids biosynthesis: toward a new category of inherited metabolic diseases.
P2860
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P2860
The enigmatic role of tafazzin in cardiolipin metabolism
description
2009 nî lūn-bûn
@nan
2009 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2009 թվականի հոտեմբերին հրատարակված գիտական հոդված
@hy
2009年の論文
@ja
2009年論文
@yue
2009年論文
@zh-hant
2009年論文
@zh-hk
2009年論文
@zh-mo
2009年論文
@zh-tw
2009年论文
@wuu
name
The enigmatic role of tafazzin in cardiolipin metabolism
@ast
The enigmatic role of tafazzin in cardiolipin metabolism
@en
The enigmatic role of tafazzin in cardiolipin metabolism
@nl
type
label
The enigmatic role of tafazzin in cardiolipin metabolism
@ast
The enigmatic role of tafazzin in cardiolipin metabolism
@en
The enigmatic role of tafazzin in cardiolipin metabolism
@nl
prefLabel
The enigmatic role of tafazzin in cardiolipin metabolism
@ast
The enigmatic role of tafazzin in cardiolipin metabolism
@en
The enigmatic role of tafazzin in cardiolipin metabolism
@nl
P2093
P1476
The enigmatic role of tafazzin in cardiolipin metabolism
@en
P2093
Bwee Tien Poll-The
Celia Pérez-Cerdá
Daniela Karall
Frédéric M Vaz
Marjolein Turkenburg
Ronald J Wanders
Sabrina Malvagia
Willem Kulik
P304
P356
10.1016/J.BBAMEM.2009.07.009
P407
P577
2009-07-18T00:00:00Z