The enigmatic role of tafazzin in cardiolipin metabolism - Test2 - elhamkhani - TriplyDB

The enigmatic role of tafazzin in cardiolipin metabolism

The enigmatic role of tafazzin in cardiolipin metabolism

http://www.wikidata.org/entity/Q28252517

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Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation Mitochondria targeting of non-peroxidizable triphenylphosphonium conjugated oleic acid protects mouse embryonic cells against apoptosis: role of cardiolipin remodeling Cardiac and skeletal muscle defects in a mouse model of human Barth syndrome Making heads or tails of phospholipids in mitochondria Barth Syndrome: From Mitochondrial Dysfunctions Associated with Aberrant Production of Reactive Oxygen Species to Pluripotent Stem Cell Studies Successful management of Barth syndrome: a systematic review highlighting the importance of a flexible and multidisciplinary approach Phospholipase A2 enzymes: physical structure, biological function, disease implication, chemical inhibition, and therapeutic intervention A mitochondrial phosphatase required for cardiolipin biosynthesis: the PGP phosphatase Gep4.Regulation of mitochondrial phospholipids by Ups1/PRELI-like proteins depends on proteolysis and Mdm35.LPS impairs oxygen utilization in epithelia by triggering degradation of the mitochondrial enzyme Alcat1 Defining functional classes of Barth syndrome mutation in humans Disorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genes Cardiolipin remodeling: a regulatory hub for modulating cardiolipin metabolism and function The complexity of cardiolipin in health and disease Cell biology. Metabolic control of cell death Bacteria, yeast, worms, and flies: exploiting simple model organisms to investigate human mitochondrial diseases Developmental Sex Differences in the Metabolism of Cardiolipin in Mouse Cerebral Cortex Mitochondria Dynamic simulation of cardiolipin remodeling: greasing the wheels for an interpretative approach to lipidomics.Comprehensive analysis of phospholipids and glycolipids in the opportunistic pathogen Enterococcus faecalis Tafazzin (TAZ) promotes the tumorigenicity of cervical cancer cells and inhibits apoptosis A mathematical model for the determination of steady-state cardiolipin remodeling mechanisms using lipidomic data.The 3-methylglutaconic acidurias: what's new?Modeling the mitochondrial cardiomyopathy of Barth syndrome with induced pluripotent stem cell and heart-on-chip technologies.Mutations in the phospholipid remodeling gene SERAC1 impair mitochondrial function and intracellular cholesterol trafficking and cause dystonia and deafness.CLPB mutations cause 3-methylglutaconic aciduria, progressive brain atrophy, intellectual disability, congenital neutropenia, cataracts, movement disorder Barth syndrome mutations that cause tafazzin complex lability.Manganese superoxide dismutase: guardian of the powerhouse.Improved functional recovery to I/R injury in hearts from lipocalin-2 deficiency mice: restoration of mitochondrial function and phospholipids remodeling Turnover of nonessential fatty acids in cardiolipin from the rat heart.Mouse Tafazzin Is Required for Male Germ Cell Meiosis and Spermatogenesis.Myocardial regulation of lipidomic flux by cardiolipin synthase: setting the beat for bioenergetic efficiency.Tafazzin knockdown in mice leads to a developmental cardiomyopathy with early diastolic dysfunction preceding myocardial noncompaction.New clinical and molecular insights on Barth syndrome Intra-individual plasticity of the TAZ gene leading to different heritable mutations in siblings with Barth syndrome Dysfunctional cardiac mitochondrial bioenergetic, lipidomic, and signaling in a murine model of Barth syndrome Left ventricular noncompaction (LVNC) and low mitochondrial membrane potential are specific for Barth syndrome.Unremodeled and remodeled cardiolipin are functionally indistinguishable in yeast.Formation and regulation of mitochondrial membranes.Cardiological manifestations of mitochondrial respiratory chain disorders.Disorders of phospholipids, sphingolipids and fatty acids biosynthesis: toward a new category of inherited metabolic diseases.

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P2860

The enigmatic role of tafazzin in cardiolipin metabolism

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description

2009 nî lūn-bûn

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2009 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած

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2009年の論文

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2009年論文

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The enigmatic role of tafazzin in cardiolipin metabolism

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The enigmatic role of tafazzin in cardiolipin metabolism

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The enigmatic role of tafazzin in cardiolipin metabolism

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J.BBAMEM.2009.07.009

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Biochimica et Biophysica Acta

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Bwee Tien Poll-The

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Celia Pérez-Cerdá

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Daniela Karall

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2003-2014

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Riekelt H Houtkooper

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